罕少疾病杂志
罕少疾病雜誌
한소질병잡지
JOURNAL OF RARE AND UNCOMMON DISEASES
2014年
3期
1-4
,共4页
张文丽%钟凤鸾%许蕾%张红宇
張文麗%鐘鳳鸞%許蕾%張紅宇
장문려%종봉란%허뢰%장홍우
EB病毒%慢性活动性EBV感染%EB病毒相关的T/NK细胞淋巴增殖性疾病%EB病毒相关淋巴瘤%诊断
EB病毒%慢性活動性EBV感染%EB病毒相關的T/NK細胞淋巴增殖性疾病%EB病毒相關淋巴瘤%診斷
EB병독%만성활동성EBV감염%EB병독상관적T/NK세포림파증식성질병%EB병독상관림파류%진단
Epstein-Barr Virus%Chronic Active EBV Infection(CAEBV)%EBV Associated T/NK-cell Lymphoproliferative Disease%EBV Associated Lymphoma%Diagnosis
EBV+T/NK-LPD在成年人发病少见,大部分病程呈暴发性,预后极差。疾病无特征性临床表现及病理组织学改变,不易诊断。本文就成年人EBV相关的T/NK细胞淋巴增殖病的诊断做探讨,讨论的问题包括EBV感染活动标志、细胞因子的表达和EBV克隆性扩增。
EBV+T/NK-LPD在成年人髮病少見,大部分病程呈暴髮性,預後極差。疾病無特徵性臨床錶現及病理組織學改變,不易診斷。本文就成年人EBV相關的T/NK細胞淋巴增殖病的診斷做探討,討論的問題包括EBV感染活動標誌、細胞因子的錶達和EBV剋隆性擴增。
EBV+T/NK-LPD재성년인발병소견,대부분병정정폭발성,예후겁차。질병무특정성림상표현급병리조직학개변,불역진단。본문취성년인EBV상관적T/NK세포림파증식병적진단주탐토,토론적문제포괄EBV감염활동표지、세포인자적표체화EBV극륭성확증。
Adult EBV associated T/NK-cell lymphoproliferative disease is a rare disease, the majority of patients with fulminant course and poor prognosis.Because of the lack of characteristics clinical manifestations and pathological histology change,it is not easy to diagnosis. The article discuss the diagnosis of adult EBV associated T/NK-cell lymphoproliferative disease,reviews the EBV infection sign,cytokine and EBV cloned amplification.