中华小儿外科杂志
中華小兒外科雜誌
중화소인외과잡지
CHINESE JOURNAL OF PEDIATRIC SURGERY
2012年
3期
210-213
,共4页
崔勇%王滨%邵广瑞%王若义%张伟
崔勇%王濱%邵廣瑞%王若義%張偉
최용%왕빈%소엄서%왕약의%장위
消化系统畸形%排便障碍%磁共振成像
消化繫統畸形%排便障礙%磁共振成像
소화계통기형%배편장애%자공진성상
Digestive system abnormalities%Defecatory dysfunction%Magnetic resonance imaging
目的 提高对MRI诊断肛直肠畸形术后排便障碍价值的认识,为进一步治疗提供参考.方法 以临床检查及术中所见为参照,回顾性分析2009年8月至2011年7月34例肛直肠畸形术后排便障碍患儿的MR图像,分别评价其术后肛直肠的形态及位置、盆底肌的发育状况及伴随的术后改变.结果 在21例先天性肛门闭锁、4例Currarino三联症和2例泄殖腔畸形术后排便障碍的患儿中,发现25例盆底肌发育不良,其中21例合并骶尾骨发育不良;21例肛门及直肠周围广泛瘢痕形成;14例直肠扩张,其中3例合并直肠后突,2例合并直肠前突;直肠狭窄6例;8例并发腹膜脂肪疝;6例肛直角增大;3例直肠下段偏移,2例未位于括约肌复合体环内;以前手术遗漏直肠尿道瘘3例;脊髓栓系4例.而在6例先天性巨结肠及1例乙状结肠闭锁术后发生排便困难的患儿中,盆底肌及骶尾骨均发育良好;6例表现为直肠轻中度扩张;1例腹膜脂肪疝.结论 MRI对于肛直肠畸形术后排便障碍的患儿具有重要应用价值,能对进一步治疗及预后提供可靠信息.
目的 提高對MRI診斷肛直腸畸形術後排便障礙價值的認識,為進一步治療提供參攷.方法 以臨床檢查及術中所見為參照,迴顧性分析2009年8月至2011年7月34例肛直腸畸形術後排便障礙患兒的MR圖像,分彆評價其術後肛直腸的形態及位置、盆底肌的髮育狀況及伴隨的術後改變.結果 在21例先天性肛門閉鎖、4例Currarino三聯癥和2例洩殖腔畸形術後排便障礙的患兒中,髮現25例盆底肌髮育不良,其中21例閤併骶尾骨髮育不良;21例肛門及直腸週圍廣汎瘢痕形成;14例直腸擴張,其中3例閤併直腸後突,2例閤併直腸前突;直腸狹窄6例;8例併髮腹膜脂肪疝;6例肛直角增大;3例直腸下段偏移,2例未位于括約肌複閤體環內;以前手術遺漏直腸尿道瘺3例;脊髓栓繫4例.而在6例先天性巨結腸及1例乙狀結腸閉鎖術後髮生排便睏難的患兒中,盆底肌及骶尾骨均髮育良好;6例錶現為直腸輕中度擴張;1例腹膜脂肪疝.結論 MRI對于肛直腸畸形術後排便障礙的患兒具有重要應用價值,能對進一步治療及預後提供可靠信息.
목적 제고대MRI진단항직장기형술후배편장애개치적인식,위진일보치료제공삼고.방법 이림상검사급술중소견위삼조,회고성분석2009년8월지2011년7월34례항직장기형술후배편장애환인적MR도상,분별평개기술후항직장적형태급위치、분저기적발육상황급반수적술후개변.결과 재21례선천성항문폐쇄、4례Currarino삼련증화2례설식강기형술후배편장애적환인중,발현25례분저기발육불량,기중21례합병저미골발육불량;21례항문급직장주위엄범반흔형성;14례직장확장,기중3례합병직장후돌,2례합병직장전돌;직장협착6례;8례병발복막지방산;6례항직각증대;3례직장하단편이,2례미위우괄약기복합체배내;이전수술유루직장뇨도루3례;척수전계4례.이재6례선천성거결장급1례을상결장폐쇄술후발생배편곤난적환인중,분저기급저미골균발육량호;6례표현위직장경중도확장;1례복막지방산.결론 MRI대우항직장기형술후배편장애적환인구유중요응용개치,능대진일보치료급예후제공가고신식.
Objective To assess the value of MRI in postoperative defecatory dysfunction after anorectal malformation (ARM) procedure, and provide further experiences for following studies. Methods MRI findings from 34 patients with postoperative defecatory dysfunction after ARM procedure were targeted and retrospective analysis was conduced to evaluate the postoperative morphology of anorectum、developmental status of pelvic floor musculature and other associated pathological changes. Results All patients included 21 cases with congenital imperforate anus, 4 cases with Currarino syndrome and 2 with cloaca malformation. Among them dysplasia of pelvic floor musculature could be found in 25 cases, 21 cases were associated with sacral deficiency, severe scar around anus and rectum were seen in them; Furthermore, 14 cases of rectal dilations and 3 cases of posterior rectoceles, as well as 2 cases of anterior rectoceles were also found; 6 cases of rectal stenosis, 8 cases of peritoneal fat hernias and 6 cases associated with increased anorectal angles were observed; Moreover, 3 cases of lower displacement of rectum and 2 of them dislocated from sphincter complex; Among all 3 cases was caused due to omitting of pre-exist recto-urethral fistulas and 4 case of tethered cords were presented on MR images. However, better development of pelvic floor musculature and sacrum were seen in 6 cased of HSCR and 1 case of sigmoid atresia respectively, although they presented mild-moderate rectal dilation and 1 of them was associated with peritoneal fat hernia. Conclusions MRI played important roles in formation provision for ARM postoperative defecatory dysfunction populations.