CAJ | 학술논문

目的探讨Sturge-Weber综合征的病理变化和CT、MRI表现特征,评价其诊断价值.方法回顾分析15例Sturge-Weber综合征的临床及影像学资料.所有病例均行常规螺旋CT扫描,其中2例有面部三叉神经分布区皮肤血管瘤的患儿,CT扫描未见异常,而进行MRI增强检查.结果 15例CT图像中,13例平扫显示患侧皮层钙化,其中轻度钙化4例,中度钙化8例,重度钙化1例;2例无钙化.2例MRI增强图像中,显示皮层下脑回状强化及软脑膜血管瘤1例;显示侧脑室脉络从增大,室管膜下静脉扩张及深静脉血管团1例.所有患者均有不同程度脑萎缩,其中6例受累脑灰白质不清;侧室脉络从增大4例;颅盖板障增厚6例.结论脑叶皮层下"脑回样"钙化是Sturge-Weber综合征的特征性表现,CT和MRI是诊断该病的主要检查手段,MRI增强扫描确诊早期Sturge-Weber 综合征有一定价值.
목적 탐토Sturge-Weber종합정적병리변화화CT、MRI표현특정,평개기진단개치.방법 회고분석15례Sturge-Weber종합정적림상급영상학자료.소유병례균행상규라선CT소묘,기중2례유면부삼차신경분포구피부혈관류적환인,CT소묘미견이상,이진행MRI증강검사.결과 15례CT도상중,13례평소현시환측피층개화,기중경도개화4례,중도개화8례,중도개화1례;2례무개화.2례MRI증강도상중,현시피층하뇌회상강화급연뇌막혈관류1례;현시측뇌실맥락종증대,실관막하정맥확장급심정맥혈관단1례.소유환자균유불동정도뇌위축,기중6례수루뇌회백질불청;측실맥락종증대4례;로개판장증후6례.결론 뇌협피층하"뇌회양"개화시Sturge-Weber종합정적특정성표현,CT화MRI시진단해병적주요검사수단,MRI증강소묘학진조기Sturge-Weber 종합정유일정개치.
Objective To discuss the pathologic change of sturge-weber syndrome and the manifestation features of CT and MRI to estimate its diagnostic value. Methods Retrospecting and analyzing the clinical and imaging materials of 15 Sturge-Weber syndrome. All patients underwent conventional spiral CT scans of which 2 patients with facial vascular nerves angioma in the trigeminal nerve distribution to find no abnormality so we used MRI enhancing check.Results Among 15 CT images, 13plain scans showed cortical calcification in affected side of which there were 4 with light calcification, 8 with medium calcification, 1 with heavy calcification and 2 with no calcification. In 2 MRI enhancing images,one showed the subcortical gyriform enhancement and the pia mater haemangioma and the other one showed choroids plexus enlargement of lateral venicles, dilated subependymal veins and deep vein vasvular. And all patients had cerebral atrophy in variouds degrees of which there were 6 troubled by unclear encephalon ray matter, 4 with choroids plexus enlargement of lateral ventricles and 6 with crania diploetic prominence.Conclusion The lobe subcortical calcification of"gyriform" is the characteristic manifestation of SturgeWeber syndrome and CT and MRI are the main checking means and it is valuable to use MRI enhancing scans to make a definite diagnosis of early Sturge-Weber syndrome.