CAJ | 학술논문

目的探讨几种罕少见的脑胚胎性肿瘤的临床病理特征及影像表现.方法回顾性分析10例罕少见的经手术病理证实为脑胚胎性肿瘤患者的临床病理特征及MRI、CT表现.结果10例中,幕上原始神经外胚层肿瘤6例,室管膜母细胞瘤2例,髓上皮瘤1例,非典型性畸胎样或横纹肌样瘤1例,其中,4例为婴幼儿和儿童.各肿瘤的病理组织学表现具有一定特征性,是确诊的依据.肿瘤均位于幕上,体积较大,形态多不规则,呈分叶状,信号、密度不均匀,坏死囊变多见;肿瘤实质CT平扫多旱稍高密度,MRI表现为T2WI呈等或较高信号,T1WI呈较低信号,增强扫描显著强化.结论罕少见脑胚胎性肿瘤患者的MRI、CT表现无明显特异性,结合临床及病理组织学特征对其进行全面认识了解十分必要.
목적 탐토궤충한소견적뇌배태성종류적림상병리특정급영상표현.방법 회고성분석10례한소견적경수술병리증실위뇌배태성종류환자적림상병리특정급MRI、CT표현.결과10례중,막상원시신경외배층종류6례,실관막모세포류2례,수상피류1례,비전형성기태양혹횡문기양류1례,기중,4례위영유인화인동.각종류적병리조직학표현구유일정특정성,시학진적의거.종류균위우막상,체적교대,형태다불규칙,정분협상,신호、밀도불균균,배사낭변다견;종류실질CT평소다한초고밀도,MRI표현위T2WI정등혹교고신호,T1WI정교저신호,증강소묘현저강화.결론한소견뇌배태성종류환자적MRI、CT표현무명현특이성,결합림상급병리조직학특정대기진행전면인식료해십분필요.
Objective To investigate the clinicopathologic features and imaging findings of several kinds of rare and uncommon brain embryonal tumours. Methods MRI or CT appearance and clinicopathologic features in 10 eases of histopathology confirmed brain embryonal tumours were retrospectively analyzed.Results Among 10 cases,there were supratentorial primitive neuroectodermal tumour(sPNET) in 6,ependymoblastoma in 2,medulloepithelioma and atypical teratoid/rhabdoid tumour (AT/RT)in 1 respectively.Patients in 4 cases were infancy and childhood.There was characteristic of the clinicopathologic features of tumors that were the evidence of accurate diagnosis. All lesions were located in the supratentorial region.The tumors were large,usually lobulated in shape irregularly and showed heterogeneous density or signal intensity with some cystic and necrotic areas.The tumors parenchyma appeared slightly high density on CT imaging,iso-or high signal on T2WI and slight low signal on T1WI with intense enhancement after contrast injection.Conclusion MRI or CT findings of rare and uncommon brain embryonal tumours were not characteristic,it Was very essential to know the tumors combined with the clinical and pathologic features.