CAJ | 학술논문

目的探讨非典型畸胎样横纹肌样瘤(AT/RT)的临床特点、诊断及治疗方法,以提高对该疾病认识.方法回顾性分析本科经治且病理证实的1例患者的临床资料,并总结分析国内外此类疾病相关报道及研究.结果患者行手术治疗后术前剧烈头痛症状明显缓解,无手术相关并发症,出院后未行术后放化疗,随访患者5个月后死亡.结论 AT/RT比较罕见,该类患者预后差,复发率及死亡率高,术后辅助放化疗能改善患者预后.
목적 탐토비전형기태양횡문기양류(AT/RT)적림상특점、진단급치료방법,이제고대해질병인식.방법 회고성분석본과경치차병리증실적1례환자적림상자료,병총결분석국내외차류질병상관보도급연구.결과 환자행수술치료후술전극렬두통증상명현완해,무수술상관병발증,출원후미행술후방화료,수방환자5개월후사망.결론 AT/RT비교한견,해류환자예후차,복발솔급사망솔고,술후보조방화료능개선환자예후.
Objective To improve the cognition of the disease by exploring the clinical feature,diagnosis and therapeutic method of Atypical teratoid/rhabdoid tumors (AT/RT).Method Clinical data of one patient diagnosed AT/RT by postoperative pathology was studied retrospectively,domestic and foreign related reports and studies of such disease were reviewed.Results The symptom of severe headache was obviously alleviated after surgical treatment,the patient followed- up abandoned postoperative radiation and chemotherapy and died after 5 months postoperatively.Conclusions AT/RT is a rare disease with poor prognosis,high recurrence and mortality.Postoperative adjuvant chemotherapy and radiation can improve the prognosis of patients.