中华皮肤科杂志
中華皮膚科雜誌
중화피부과잡지
Chinese Journal of Dermatology
2008年
6期
361-363
,共3页
赵丽%叶静%李存江%孙燕妮%佟长顺
趙麗%葉靜%李存江%孫燕妮%佟長順
조려%협정%리존강%손연니%동장순
结节性硬化症%皮肤表现%发病年龄
結節性硬化癥%皮膚錶現%髮病年齡
결절성경화증%피부표현%발병년령
Tuberous sclerosis%Skin manifestation%Age of onset
目的 探讨结节性硬化症皮肤皮损特点及首发年龄特点.方法 收集并分析54例结节性硬化症皮损资料.结果 血管纤维瘤的出现率为72.5%,发病年龄的中位数为7岁,1～9岁为高峰期;甲周纤维瘤的出现率为26%,发病年龄的中位数为14岁,10～19岁为高峰期;色素脱失斑的出现率为70%,发病年龄的中位数为0.2岁,1岁以内为高峰期;鲨鱼皮斑的出现率为48%,发病年龄的中位数为6岁,1～9岁为高峰期.结论 结节性硬化症的皮损发生率高,多在幼年发病.
目的 探討結節性硬化癥皮膚皮損特點及首髮年齡特點.方法 收集併分析54例結節性硬化癥皮損資料.結果 血管纖維瘤的齣現率為72.5%,髮病年齡的中位數為7歲,1～9歲為高峰期;甲週纖維瘤的齣現率為26%,髮病年齡的中位數為14歲,10～19歲為高峰期;色素脫失斑的齣現率為70%,髮病年齡的中位數為0.2歲,1歲以內為高峰期;鯊魚皮斑的齣現率為48%,髮病年齡的中位數為6歲,1～9歲為高峰期.結論 結節性硬化癥的皮損髮生率高,多在幼年髮病.
목적 탐토결절성경화증피부피손특점급수발년령특점.방법 수집병분석54례결절성경화증피손자료.결과 혈관섬유류적출현솔위72.5%,발병년령적중위수위7세,1～9세위고봉기;갑주섬유류적출현솔위26%,발병년령적중위수위14세,10～19세위고봉기;색소탈실반적출현솔위70%,발병년령적중위수위0.2세,1세이내위고봉기;사어피반적출현솔위48%,발병년령적중위수위6세,1～9세위고봉기.결론 결절성경화증적피손발생솔고,다재유년발병.
Objective To analyze the features of cutaneous lesions and age of onset of tuberous sclerosis(TS).Methods A total of 54 TS patients were recruited;their clinical data were analysed.Results The occurance of facial angiofibromas,periungual fibromas,hypomelanotic macules and shark macules was 72.5%,26%,70%and 48%,respectively,and the median age of onset of these lesions was 7,14,0.2 and 6 years,respectively,with a peak at 1-9,10-19,＜1 and 1-9 years,respectively.Conclusions Cutaneous lesions are commonly seen in TS,and most of them develop early in life.
