CAJ | 학술논문

副神经节瘤是一类起源于胚胎神经嵴细胞的非常少见的软组织神经内分泌肿瘤,原发于肾脏的恶性副神经节瘤极为罕见.本文报道1例原发于肾脏的恶性副神经节瘤.患者为女性55岁,患者因顽固性咳嗽、CT检查发现左肺内实性肿物而入院,入院后腹部超声显示左肾占位.行左肾和肿物全切除术,术后病理组织学证实肿瘤为来源于肾脏的恶性副神经节瘤.术后对病人随访了12个月,目前病人一般情况良好,超声检查未见复发征象.基于本病例资料,结合文献报道,探讨影像学检查对本病的诊断和临床意义.
부신경절류시일류기원우배태신경척세포적비상소견적연조직신경내분비종류,원발우신장적악성부신경절류겁위한견.본문보도1례원발우신장적악성부신경절류.환자위녀성55세,환자인완고성해수、CT검사발현좌폐내실성종물이입원,입원후복부초성현시좌신점위.행좌신화종물전절제술,술후병리조직학증실종류위래원우신장적악성부신경절류.술후대병인수방료12개월,목전병인일반정황량호,초성검사미견복발정상.기우본병례자료,결합문헌보도,탐토영상학검사대본병적진단화림상의의.
Paraganglioma is a rare neuroendocrine tumor arising from the undifferentiated cells of the primitive neural crest.We report a case of malignant paraganglioma originating from the left kidney.The 55-year-old female patient was admitted for intractable cough for a month and the presence of a solid mass in the left lung detected by computer tomography(CT).Sonography revealed a mass in the left kidney after admission.Complete surgical resection of the tumor was performed and the diagnosis of malignant paraganglioma originating from the left kidney was established pathologically.During the follow-up for 12 months,the patient showed a good general condition and sonography revealed no evidence of recurrence.Based on these findings,we discussed the diagnosis of this disease using medical imaging modalities.