CAJ | 학술논문

门静脉海绵样变性约占小儿门静脉高压的40％.与其他引起门静脉高压的病种相比,该病有发病年龄早、出血危险性高及肝功能大致正常等特点.由于病因相对单一,大多数患儿无合并其他疾病,因此合理的治疗对该病的预后有决定性意义.目前对于该病的诊疗理念国内外存在较大差异,国内仍将治疗目的主要集中在控制消化道出血方面,而国外对于该病的治疗则放在术后患儿肝脏血流灌注的改善、脾功能亢进的缓解、术后生活质量等方面,本文旨在总结近几年国外相关文献,介绍目前国外对于该病的最新研究成果.
문정맥해면양변성약점소인문정맥고압적40％.여기타인기문정맥고압적병충상비,해병유발병년령조、출혈위험성고급간공능대치정상등특점.유우병인상대단일,대다수환인무합병기타질병,인차합리적치료대해병적예후유결정성의의.목전대우해병적진료이념국내외존재교대차이,국내잉장치료목적주요집중재공제소화도출혈방면,이국외대우해병적치료칙방재술후환인간장혈류관주적개선、비공능항진적완해、술후생활질량등방면,본문지재총결근궤년국외상관문헌,개소목전국외대우해병적최신연구성과.
Cavernous transformation of portal vein accounts for about 40％ in children portal hypertension.Compared with other causes of portal hypertension disease cavernous transformation of portal vein presents early age of disease onset,high risk of bleeding and normal liver function.Because the pathology is relatively simple and most children have no other diseases,so a reasonable treatment of the disease has decisive significance.The current concept for diagnosis and treatment of the disease is different between home and abroad,Controlling upper gastrointestinal bleeding is the main purpose in out country.Reliving hypersplenism,improving liver blood supply and quality of life are much important abroad,The article aims to summarize latest foreign literature to introduce latest research for the disease abroad.