CAJ | 학술논문

风湿性疾病是一类通过自身免疫反应导致机体损伤的疾病,可累及全身各个组织器官,其中呼吸系统受累极为常见,肺间质改变是肺部受累的重要临床表现.儿童风湿性疾病相关性肺间质病变相对于成年人较少见,但肺部病变明显增加患儿的病死率,因此提高对儿童风湿性疾病相关性肺间质病变的认识,早期诊断、早期治疗对患儿预后具有很大的影响.
풍습성질병시일류통과자신면역반응도치궤체손상적질병,가루급전신각개조직기관,기중호흡계통수루겁위상견,폐간질개변시폐부수루적중요림상표현.인동풍습성질병상관성폐간질병변상대우성년인교소견,단폐부병변명현증가환인적병사솔,인차제고대인동풍습성질병상관성폐간질병변적인식,조기진단、조기치료대환인예후구유흔대적영향.
Rheumatic disease is a kind of autoimmune disease,which can damage all of tissues and organ,the respiratory system is commonly involved.Interstitial lung disease(ILD) is the most prevalent respiratory manifestation.ILD of unknown etiology in immunocompetent patients is rare in children,but it can increase the mortality obviously.Therefore,we should improve the knowledge of rheumatic diseases-ILD,earlier diagnosis and treatment are very important for the life quality of children.