CAJ | 학술논문

自身免疫多腺体综合征系指同一个体有2个或2个以上内分泌腺体在自身免疫性炎症侵袭下先后或间时发生功能减退,亦可累及其他非内分泌系统.根据疾病的起病年龄、临床特征及遗传特性,将自身免疫多腺体综合征分为4型.由于症状呈序贯性发生,临床各型的拟诊多在儿科完成.治疗原则是综合分析、替代治疗和主次兼顾.
자신면역다선체종합정계지동일개체유2개혹2개이상내분비선체재자신면역성염증침습하선후혹간시발생공능감퇴,역가루급기타비내분비계통.근거질병적기병년령、림상특정급유전특성,장자신면역다선체종합정분위4형.유우증상정서관성발생,림상각형적의진다재인과완성.치료원칙시종합분석、체대치료화주차겸고.
Polyglandular autoimmune syndromes (PAS) comprises a wide spectrum of autoimmune disorders for autoimmune inflammatory to invade.According to age of presentation,characteristic patterns of disease combinations,and different modes of inheritance,PAS are classified into four subtypes.Actual diagnosis of PAS involves clinical syndromes,serological measurement of organ-specific autoantibodies and subsequent functional testing.Principles of treatment included comprehensive assessment,hormone replacement,general consideration.