中华全科医师杂志
中華全科醫師雜誌
중화전과의사잡지
CHINESE JOURNAL OF GENERAL PRACTITIONERS
2010年
9期
642-644
,共3页
迟克强%毛定安%李介民%刘利群
遲剋彊%毛定安%李介民%劉利群
지극강%모정안%리개민%류리군
丹迪-沃克综合征%诊断
丹迪-沃剋綜閤徵%診斷
단적-옥극종합정%진단
Dandy-Walker Syndrome%Diagnosis
结合文献对本院2006年5月至2009年11月经头颅MRI诊断为丹迪-沃克综合征的5例患者的临床资料进行分析.结果 显示,该病临床特点以运动发育迟缓和小脑体征多见,5例中3例伴有小脑体征.多在儿童期发病.头颅影像学检查表现为第四脑室扩大,小脑蚓部体积变小或缺如.MRI是诊断丹迪-沃克综合征的最佳辅助检查方法.
結閤文獻對本院2006年5月至2009年11月經頭顱MRI診斷為丹迪-沃剋綜閤徵的5例患者的臨床資料進行分析.結果 顯示,該病臨床特點以運動髮育遲緩和小腦體徵多見,5例中3例伴有小腦體徵.多在兒童期髮病.頭顱影像學檢查錶現為第四腦室擴大,小腦蚓部體積變小或缺如.MRI是診斷丹迪-沃剋綜閤徵的最佳輔助檢查方法.
결합문헌대본원2006년5월지2009년11월경두로MRI진단위단적-옥극종합정적5례환자적림상자료진행분석.결과 현시,해병림상특점이운동발육지완화소뇌체정다견,5례중3례반유소뇌체정.다재인동기발병.두로영상학검사표현위제사뇌실확대,소뇌인부체적변소혹결여.MRI시진단단적-옥극종합정적최가보조검사방법.
5 cases diagnosed with Dandy-Walker Syndrome from May 2006 to November 2009 were investigated and relevant literature reviewed. Dandy-Walker Syndrome was characterized by retarded motordevelopment and cerebellar signs. The latter was observed in 3 cases in our series. The disorder, mostly influencing childhood, typically causes the fourth ventricle enlarged, and the cauda cerebelli atrophic or even absent. MRI is the most optimal radiological method to diagnose it.