CAJ | 학술논문

目的总结肝脏未分化胚胎性肉瘤(UESL)的临床病理学特点.方法对11年来第二军医大学东方肝胆外科医院手术切除的9例UESL病人的临床资料进行回顾性分析.结果该组9例年龄5～63岁,其中6例年龄5～10岁;肿瘤长径平均15.1 cm.术前6例误诊为肝囊腺瘤(癌),2例误诊为原发性肝癌,1例误诊为肝良性囊性占位,病理学检查均证实为未分化胚胎性肉瘤.结论 UESL为少见高度恶性肿瘤;CT与B超表现的不一致性为本病的重要特点;治疗上目前仍以手术切除肿瘤为首选,手术前后联合化疗及放疗等综合治疗可提高疗效.
목적 총결간장미분화배태성육류(UESL)적림상병이학특점.방법 대11년래제이군의대학동방간담외과의원수술절제적9례UESL병인적림상자료진행회고성분석.결과 해조9례년령5～63세,기중6례년령5～10세;종류장경평균15.1 cm.술전6례오진위간낭선류(암),2례오진위원발성간암,1례오진위간량성낭성점위,병이학검사균증실위미분화배태성육류.결론 UESL위소견고도악성종류;CT여B초표현적불일치성위본병적중요특점;치료상목전잉이수술절제종류위수선,수술전후연합화료급방료등종합치료가제고료효.
Objective To investigate the clinicopathological features of undifferentiated embryo-nal sarcoma of the liver (UESL). Methods The clinical data of 9 UESL cases treated in our hospital between 1996 and 2007 were retrospectively analyzed. Results The patients were children and young adults. Clinical presentation was typically an abdominal mass that may be accompanied by pain and fe-ver. Tumors were all removed surgically in the 9 patients. Conclusion UESL is an unusual malignan-cy of the liver. Discrepancy of internal architecture between US and CT is one of the important charac-teristic of UESL. Whenever feasible, surgical resection should be attempted as a part of combination modalities. Modern rnultimodal treatment and supportive therapy might promote the survival rate.