CAJ | 학술논문

大疱性类天疱疮是一获得性自身免疫性疾病.常累及老年人,儿童少见.儿童大疱性类天疱疮的发病率无明显的人种、性别区别,年龄跨度较大,儿童期各年龄组均有报道.儿童大疱性类天疱疮的诊断主要依据临床表现、组织病理及直接免疫荧光检查.在病因及临床表现上儿童有别于成人,但在组织病理及直接免疫荧光上与成人大疱性类天疱疮相似.
대포성류천포창시일획득성자신면역성질병.상루급노년인,인동소견.인동대포성류천포창적발병솔무명현적인충、성별구별,년령과도교대,인동기각년령조균유보도.인동대포성류천포창적진단주요의거림상표현、조직병리급직접면역형광검사.재병인급림상표현상인동유별우성인,단재조직병리급직접면역형광상여성인대포성류천포창상사.
Bullous pemphigoid (BP) is an acquired,chronic,autoimmune bullous disease that usually affects the elderly but rarely children.No predilection for race or gender is recognized for childhood BP.The age of onset is variable.and there have been case reports in all age groups during childhood.The diagnosis of childhood BP is mainly based on clinical.histological and direct immunoffuoreseence findings.Although pathological and direct immunofluoreseence findings ale similar between childhood and adult BP,but their etiology and clinical features are different.