CAJ | 학술논문

目的追踪1例婴儿颅骨肌纤维瘤病患者，探讨其自然病程、手术疗效及预后。方法8个月女孩因发现左颞及右枕部颅骨两处肿物入院，在我院行左颞肿物全切除，术后病理确诊为婴儿肌纤维瘤病。右枕部颅骨病灶未手术而给予随访观察。术后半年、1年、2年、4年分别行影像学检查，观察其自然病程。结果术后半年额骨近中线处出现一新病灶，右枕部病灶部分性消退，术后2年所有病灶均完全消退，目前患儿生长发育正常。结论发生于颅骨的婴儿肌纤维瘤病罕见，有自发消退倾向，应重新正确认识此病并给予正确的治疗。
목적 추종1례영인로골기섬유류병환자，탐토기자연병정、수술료효급예후。방법8개월녀해인발현좌섭급우침부로골량처종물입원，재아원행좌섭종물전절제，술후병리학진위영인기섬유류병。우침부로골병조미수술이급여수방관찰。술후반년、1년、2년、4년분별행영상학검사，관찰기자연병정。결과술후반년액골근중선처출현일신병조，우침부병조부분성소퇴，술후2년소유병조균완전소퇴，목전환인생장발육정상。결론발생우로골적영인기섬유류병한견，유자발소퇴경향，응중신정학인식차병병급여정학적치료。
Objective We present a case of multicentre infantile myofibromatosis with involvement exclusively of the skull. Method An 8 - month - old girl presented with left temporal and right occipital calvarial lesions was underwent total resection of the temporal mass. The histopathological study gave a diagnosis of infantile myofibromatosis. The other lesion was left untreated. Serial follow - up by neuroimaging was obtained to explore the natural history of the disease. Results Six months after surgery, a new lesion in the midline of frontal bone was found and there was partial regression of the occipital lesion. Complete regression of the untreated lesions was shown at 2 years after operation. Conclusions Based on our case and literature review,we believe the multicentre infantile myofibromatosis of the skull is a disease of spontaneous regression.