中华眼科杂志
中華眼科雜誌
중화안과잡지
Chinese Journal of Ophthalmology
2008年
1期
46-49
,共4页
于伟泓%董方田%李静贞%毛进
于偉泓%董方田%李靜貞%毛進
우위홍%동방전%리정정%모진
无虹膜%视觉,双眼%治疗结果
無虹膜%視覺,雙眼%治療結果
무홍막%시각,쌍안%치료결과
Aniridia%Vision,binocular%Treatment outcome
目的 探讨先天性无虹膜患者的临床表现及其治疗.方法 为回顾性系列病例研究.选择1984年1月至2007年1月于我科就诊的8例(16只眼)先天性无虹膜患者,均为双眼患病,矫正视力均低于1.0.8例患者均伴不同程度白内障;其中5只眼伴青光眼,均为难治性青光眼;4只眼伴弱视;8只眼伴眼球水平震颤.根据病情不同分别行囊外白内障摘除术和人工晶状体植入术、小梁切除术、睫状突激光光凝术、戴镜行弱视训练、配戴角膜接触镜等治疗.结果 6只晶状体明显混浊眼行白内障手术后视力有不同程度提高,无手术并发症.5只青光眼中,1只眼行小梁切除术,但术后眼压仍然不能控制于正常范围内,又行睫状突光凝术;3只眼仅行睫状突光凝术;1只眼局部使用降眼压药物治疗.此5只青光眼中,3只眼眼压得到控制,另2只眼仍不能控制于正常范围内.4只弱视眼经配镜、弱视训练后视力均有一定提高,2只眼配戴角膜接触镜后畏光症状得到缓解.结论 先天性无虹膜患者眼部表现多种多样,虽治疗棘手,但经适当的治疗后可改善视力和临床症状.
目的 探討先天性無虹膜患者的臨床錶現及其治療.方法 為迴顧性繫列病例研究.選擇1984年1月至2007年1月于我科就診的8例(16隻眼)先天性無虹膜患者,均為雙眼患病,矯正視力均低于1.0.8例患者均伴不同程度白內障;其中5隻眼伴青光眼,均為難治性青光眼;4隻眼伴弱視;8隻眼伴眼毬水平震顫.根據病情不同分彆行囊外白內障摘除術和人工晶狀體植入術、小樑切除術、睫狀突激光光凝術、戴鏡行弱視訓練、配戴角膜接觸鏡等治療.結果 6隻晶狀體明顯混濁眼行白內障手術後視力有不同程度提高,無手術併髮癥.5隻青光眼中,1隻眼行小樑切除術,但術後眼壓仍然不能控製于正常範圍內,又行睫狀突光凝術;3隻眼僅行睫狀突光凝術;1隻眼跼部使用降眼壓藥物治療.此5隻青光眼中,3隻眼眼壓得到控製,另2隻眼仍不能控製于正常範圍內.4隻弱視眼經配鏡、弱視訓練後視力均有一定提高,2隻眼配戴角膜接觸鏡後畏光癥狀得到緩解.結論 先天性無虹膜患者眼部錶現多種多樣,雖治療棘手,但經適噹的治療後可改善視力和臨床癥狀.
목적 탐토선천성무홍막환자적림상표현급기치료.방법 위회고성계렬병례연구.선택1984년1월지2007년1월우아과취진적8례(16지안)선천성무홍막환자,균위쌍안환병,교정시력균저우1.0.8례환자균반불동정도백내장;기중5지안반청광안,균위난치성청광안;4지안반약시;8지안반안구수평진전.근거병정불동분별행낭외백내장적제술화인공정상체식입술、소량절제술、첩상돌격광광응술、대경행약시훈련、배대각막접촉경등치료.결과 6지정상체명현혼탁안행백내장수술후시력유불동정도제고,무수술병발증.5지청광안중,1지안행소량절제술,단술후안압잉연불능공제우정상범위내,우행첩상돌광응술;3지안부행첩상돌광응술;1지안국부사용강안압약물치료.차5지청광안중,3지안안압득도공제,령2지안잉불능공제우정상범위내.4지약시안경배경、약시훈련후시력균유일정제고,2지안배대각막접촉경후외광증상득도완해.결론 선천성무홍막환자안부표현다충다양,수치료극수,단경괄당적치료후가개선시력화림상증상.
Objective To explore the various clinical features of aniridia and its treatment.Methods It was a retrospective case series.All the 8 cases of 16 aniridia patients in our department from January,1984 to January,2007 were assayed.All the patients were bilateral aniridia sufiering from abnormal vision and manifested with various degree of cataract,5 eyes manifested with refractory glaucoma,8 eyes with horizontal nystigmus.These patients underwent cataract extraction and intraocular lens implantation,trabeculectomy,ciliary process laser photoeoagulation,in some of patients glass and cover strabismus exercise,color contact lens therapy were applied.Results Vision acuity in all of patients with severe cataract were improved after cataract surgery.One glaucoma eye underwent trabeculectomy,but failed to control the IOP and then received ciliary process laser photocoagulation.Three glaucoma eyes only underwent ciliary process laser photocoagulation,1 eye received topical anti-glaucoma eye drops.The IOP of 3 eyes was controlled.However,the IOP of 2 eyes was not to be controned.Vision acuity was improved in 4 strabismus eyes after wearing glass and strabismus exercise,the symptom of photophobia was disappeared in 2 eyes after wearing a pair of color contact lens.Conclusion Although it is hard selection to select the proper treatment for aniridia,most of the cases can obtain a better vision,and relief of the symptom after proper treatment.