临床儿科杂志
臨床兒科雜誌
림상인과잡지
2013年
10期
994-997
,共4页
张艺凡%牛广华%赵高阳%郑菲%袁慧姣
張藝凡%牛廣華%趙高暘%鄭菲%袁慧姣
장예범%우엄화%조고양%정비%원혜교
新生儿狼疮%母体微嵌合%先天性心脏传导阻滞
新生兒狼瘡%母體微嵌閤%先天性心髒傳導阻滯
신생인랑창%모체미감합%선천성심장전도조체
neonatal lupus erythematosus%maternal micro-chimera%congenital heart block
综述新生儿狼疮病的流行病学、病因、临床表现、治疗、随访等,着重于近些年来对该病病因的新发现,包括抗干燥综合征A(SSA/Ro)抗体和抗干燥综合征B(SSB/La)抗体、血清素(5-HT4)、心肌细胞凋亡、钙通道、微嵌合体、遗传突变等方面。
綜述新生兒狼瘡病的流行病學、病因、臨床錶現、治療、隨訪等,著重于近些年來對該病病因的新髮現,包括抗榦燥綜閤徵A(SSA/Ro)抗體和抗榦燥綜閤徵B(SSB/La)抗體、血清素(5-HT4)、心肌細胞凋亡、鈣通道、微嵌閤體、遺傳突變等方麵。
종술신생인랑창병적류행병학、병인、림상표현、치료、수방등,착중우근사년래대해병병인적신발현,포괄항간조종합정A(SSA/Ro)항체화항간조종합정B(SSB/La)항체、혈청소(5-HT4)、심기세포조망、개통도、미감합체、유전돌변등방면。
This review summarizes the epidemiology, etiology, clinical manifestation, treatment, follow-up of neonatal lupus erythematosus with focus on new discoveries on the etiology of the disease in recent years including anti-SSA/Ro and anti-SSB/La antibodies, serotonin (5-hydroxytryptamine 4), apoptosis of cardiac cells, calcium channels, maternal micro-chimera, genetic variants, to improve clinician awareness of the disease.