CAJ | 학술논문

特发性肺含铁血黄素沉着症是一种原因不明的肺泡毛细血管出血性疾病，多发于儿童，成人发病率极低，但误诊率高、预后差、病死率高。病变进程因人而异，发病机制尚不确切，治疗措施有限且存在争议。本文报道了1例成年女性特发性含铁血黄素沉着症患者的诊治资料，同时总结复习了国内外的相关文献，以期帮助临床医师提高对成人特发性肺含铁血黄素沉着症的理解与认识。
특발성폐함철혈황소침착증시일충원인불명적폐포모세혈관출혈성질병，다발우인동，성인발병솔겁저，단오진솔고、예후차、병사솔고。병변진정인인이이，발병궤제상불학절，치료조시유한차존재쟁의。본문보도료1례성년녀성특발성함철혈황소침착증환자적진치자료，동시총결복습료국내외적상관문헌，이기방조림상의사제고대성인특발성폐함철혈황소침착증적리해여인식。
Idiopathic pulmonary hemosiderosis( IPH),a noncausal diffuse alveolar hemorrhage,often appears in children,rarely in adults,but with high misdiagnosis rate,poor prognosis and high fatality rate in adult. The disease process varies with each individual,and its pathogenesis is still unknown. Treatments for it are limited and remain disputed. This paper analyzes the clinical data of an adult woman with IPH and reviews relevant literatures both at home and abroad,to improve clini-cians′understanding and awareness about IPH.