CAJ | 학술논문

目的分析肺淋巴管肌瘤病(PLAM)的临床特征及高分辨率CT(HRCT)表现，进一步提高对该病的认识。方法回顾性分析解放军总医院2010年5月~2013年5月经临床病理证实并行HRCT检查的9例PLAM患者资料，分析其肺部HRCT特点。结果9例均以不同程度气短，进行性加重为主要临床表现。 HRCT示双肺散在或弥漫分布囊状透亮影，并可见血管影位于囊状影边缘。结论 PLAM主要临床特点为不同程度气短，进行性加重，HRCT对该病的早期诊断、鉴别诊断具有重要价值。
목적분석폐림파관기류병(PLAM)적림상특정급고분변솔CT(HRCT)표현，진일보제고대해병적인식。방법회고성분석해방군총의원2010년5월~2013년5월경림상병리증실병행HRCT검사적9례PLAM환자자료，분석기폐부HRCT특점。결과9례균이불동정도기단，진행성가중위주요림상표현。 HRCT시쌍폐산재혹미만분포낭상투량영，병가견혈관영위우낭상영변연。결론 PLAM주요림상특점위불동정도기단，진행성가중，HRCT대해병적조기진단、감별진단구유중요개치。
Objective Analysis of pulmonary lymphangioleiomyomatosis (PLAM) clinical characteristics and high resolution CT (HRCT), and further enhance the understanding of the disease. Methods Retrospective analysis of PLA General Hospital in 2010 May~2013 year 5 menstrual clinical pathology in 9 cases of PLAM data parallel HRCT inspection, analysis of the HRCT features of lung. Results 9 cases with varying degrees of shortness of breath, progressive as the main clinical manifestations. HRCT showed double lung scat ered or dif use cystic lucency shadow, and visible vessels in cystic shadow edge. Conclusion PLAM clinical features are different degrees of shortness of breath, progressive, HRCT is valuable for the early diagnosis, dif erential diagnosis.