CAJ | 학술논문

目的：探讨Hallervorden-Spatz综合征的颅脑M RI诊断价值，提高对该病的认识。方法回顾性分析2007年2月～2012年4月经临床证实为 Hallervorden-Spatz综合征的4例患者颅脑MRI资料。结果 Hallervorden-Spatz综合征颅脑M RI表现为：双侧苍白球、黑质T2 WI像对称性低信号，苍白球低信号的前内侧出现斑点状高信号，即典型的“虎眼征”。SWI像上病灶呈低信号，MRS检查可见NAA、NAA/Cr及Cho/Cr下降。结论 Hallervorden-Spatz综合征具有典型的MRI表现，MRI检查在Hallervorden-Spatz综合征中有重要的诊断价值。
목적：탐토Hallervorden-Spatz종합정적로뇌M RI진단개치，제고대해병적인식。방법회고성분석2007년2월～2012년4월경림상증실위 Hallervorden-Spatz종합정적4례환자로뇌MRI자료。결과 Hallervorden-Spatz종합정로뇌M RI표현위：쌍측창백구、흑질T2 WI상대칭성저신호，창백구저신호적전내측출현반점상고신호，즉전형적“호안정”。SWI상상병조정저신호，MRS검사가견NAA、NAA/Cr급Cho/Cr하강。결론 Hallervorden-Spatz종합정구유전형적MRI표현，MRI검사재Hallervorden-Spatz종합정중유중요적진단개치。
Objective To investigate the diagnostic value of MRI in Hallervorden-Spatz syndrome .Methods MRI data of Hallervorden-Spatz syndrome in 4 patients in our hospital from February 2007 to April 2012 were retrospectively ana-lyzed .Results The brain MRI of Hallervorden-Spatz syndrome was demonstrated abnormalities confined to the pallidum , which presented diffuse low signal intensity in SWI ,and eye-of-the-tiger sign in T2 WI .Compared with the normal brain tissue ,the NAA ,NAA/Cr ,Cho/Cr were decreased .Conclusion Hallervorden-Spatz syndrome has definite MR imaging findings ,and M RI is of important value in diagnosis of Hallervorden-Spatz syndrome .