CAJ | 학술논문

自身免疫性溶血性贫血和阵发性睡眠性血红蛋白尿都是常见的溶血性疾病，前者是由于免疫功能紊乱导致的溶血，后者则是一种获得性造血干细胞克隆性疾病，两者常单独发病，伴随或相互继发的病例也可见。在临床诊疗中，阵发性睡眠性血红蛋白尿样缺陷样缺陷的自身免疫性溶血性贫血是自免溶贫的一种特殊类型，应注意与经典阵发性睡眠性血红蛋白尿样缺陷加以区分。
자신면역성용혈성빈혈화진발성수면성혈홍단백뇨도시상견적용혈성질병，전자시유우면역공능문란도치적용혈，후자칙시일충획득성조혈간세포극륭성질병，량자상단독발병，반수혹상호계발적병례야가견。재림상진료중，진발성수면성혈홍단백뇨양결함양결함적자신면역성용혈성빈혈시자면용빈적일충특수류형，응주의여경전진발성수면성혈홍단백뇨양결함가이구분。
Both autoimmune hemolytic anemia and paroxysmal nocturnal hemoglobinuria are common hemolytic diseases. The former causes hemolysis because of immune disorder, and the latter is an acquired clonal hematologic disorder of stem cells. The two entities are often separate diseases, but can also occur concomitantly or secondary to each other. paroxysmal nocturnal haemoglobinuria-like defect-like defect is a special type of autoimmune haemolytic anaemia and should be distinguished from typical paroxysmal nocturnal haemoglobinuria-like defect.