CAJ | 학술논문

目的：探讨肺淋巴管肌瘤病的高分辨率C T （H RC T ）表现，以提高对该病的认识。方法回顾性分析17例经病理证实的肺淋巴管肌瘤病胸部HRCT表现及临床资料，所有病例肺活检前均行胸部 HRCT扫描及腹部B超检查，腹部B超发现异常病例者行腹部C T检查6例。结果17例患者均为育龄期女性，胸部H RC T均表现为两肺弥漫、大小不等圆形薄壁囊状影（17/17，100％），2例部分融合成肺大泡（2/17，11．8％），4例合并气胸（4/17，23．5％），2例伴乳糜胸（2/17，11．8％）。腹部C T检查发现2例伴双侧肾错构瘤（2/17，11．8％），1例伴右侧肾错构瘤（1/17，5．9％），1例伴子宫错构瘤（1/17，5．9％），2例伴肝脏错构瘤（2/17，11．8％），3例伴腹膜后囊性淋巴管瘤（3/17，17．6％）。结论育龄期女性，胸部HRCT表现为两肺弥漫、均匀分布的圆形薄壁囊状影，应考虑肺淋巴管肌瘤病可能。应常规行腹部CT检查，腹部CT检查发现肝肾错构瘤，腹膜后囊性淋巴管瘤可协助诊断。
목적：탐토폐림파관기류병적고분변솔C T （H RC T ）표현，이제고대해병적인식。방법회고성분석17례경병리증실적폐림파관기류병흉부HRCT표현급림상자료，소유병례폐활검전균행흉부 HRCT소묘급복부B초검사，복부B초발현이상병례자행복부C T검사6례。결과17례환자균위육령기녀성，흉부H RC T균표현위량폐미만、대소불등원형박벽낭상영（17/17，100％），2례부분융합성폐대포（2/17，11．8％），4례합병기흉（4/17，23．5％），2례반유미흉（2/17，11．8％）。복부C T검사발현2례반쌍측신착구류（2/17，11．8％），1례반우측신착구류（1/17，5．9％），1례반자궁착구류（1/17，5．9％），2례반간장착구류（2/17，11．8％），3례반복막후낭성림파관류（3/17，17．6％）。결론육령기녀성，흉부HRCT표현위량폐미만、균균분포적원형박벽낭상영，응고필폐림파관기류병가능。응상규행복부CT검사，복부CT검사발현간신착구류，복막후낭성림파관류가협조진단。
Objective To discuss high resolution CT (HRCT ) features of pulmonary lymphangioleiomyomatosis (PLAM ) and to make a futher understanding of this disease .Methods 17 patients with PLAM confirmed by pathological assessment were analyzed retrospectively for chest HRCT findings .They underwent chest high resolution CT (HRCT ) , abdominal type-B ultrasonic .Additional abdominal CT scanning was carried out in 6 cases .Results All the 17 cases were female .Chest high resolution findings included multiple diffuse lung parenchyma cysts in all cases (17/17 ,100% ) ,with some cysts coalesced together to form bullae (2/17 ,11 .8% ) or cause pneumothorax (4/17 ,23 .5% ) .Tow cases had chy-lopleura (2/17 ,11 .8% ) .Common abdominal CT findings included bilateral renal hamartoma in 2 of 17 patients and right renal hamartoma in 1 of 17 patients .One of the 17 patients had uterus hamartoma and tow cases had hepatic hamartoma and three cases had cystic lymphangioma in retroperitoneum .Conclusion If chest high resolution CT findings of child-bearing-age women included sporadic or disseminated multiple diffuse lung parenchyma cysts in bilateral lung , PLAM should be considered .As well as other routine abdominal and pelvic imaging examinations ,common abdominal CT findings showed renal hamartoma or hepatic hamartoma or cystic lymphangioma in retroperitoneum should be an important assistant effect in diagnosis .