中国医师进修杂志
中國醫師進脩雜誌
중국의사진수잡지
CHINESE JOURNAL OF POSTGRADUATES OF MEDICINE
2013年
26期
7-9
,共3页
Arnold-Chiari畸形%脊髓空洞症
Arnold-Chiari畸形%脊髓空洞癥
Arnold-Chiari기형%척수공동증
Arnold-Chiari malformation%Syringomyelia
目的 探讨Arnold-Chiari畸形I型合并脊髓空洞改良手术治疗方法及效果.方法 选择12例Arnold-Chiari畸形Ⅰ型合并脊髓空洞患者,行小脑扁桃体下疝软脑膜下切除并蛛网膜修补枕大池重建改良手术治疗,观察疗效.结果 术后第一次随访10例感觉、运动功能明显改善,2例稳定,无加重患者.第二次随访原稳定者好转2例,余患者症状无明显改变.第一次随访MRI检查显示脊髓空洞消失5例、缩小4例、无变化3例,无一例脊髓空洞扩大,3例合并脑积水者脑室明显缩小.第二次随访MRI检查与第一次随访相比无明显变化.结论 小脑扁桃体下疝软脑膜下切除并蛛网膜修补枕大池重建改良手术对Arnold-Chiari畸形Ⅰ型合并脊髓空洞治疗具有良好效果.
目的 探討Arnold-Chiari畸形I型閤併脊髓空洞改良手術治療方法及效果.方法 選擇12例Arnold-Chiari畸形Ⅰ型閤併脊髓空洞患者,行小腦扁桃體下疝軟腦膜下切除併蛛網膜脩補枕大池重建改良手術治療,觀察療效.結果 術後第一次隨訪10例感覺、運動功能明顯改善,2例穩定,無加重患者.第二次隨訪原穩定者好轉2例,餘患者癥狀無明顯改變.第一次隨訪MRI檢查顯示脊髓空洞消失5例、縮小4例、無變化3例,無一例脊髓空洞擴大,3例閤併腦積水者腦室明顯縮小.第二次隨訪MRI檢查與第一次隨訪相比無明顯變化.結論 小腦扁桃體下疝軟腦膜下切除併蛛網膜脩補枕大池重建改良手術對Arnold-Chiari畸形Ⅰ型閤併脊髓空洞治療具有良好效果.
목적 탐토Arnold-Chiari기형I형합병척수공동개량수술치료방법급효과.방법 선택12례Arnold-Chiari기형Ⅰ형합병척수공동환자,행소뇌편도체하산연뇌막하절제병주망막수보침대지중건개량수술치료,관찰료효.결과 술후제일차수방10례감각、운동공능명현개선,2례은정,무가중환자.제이차수방원은정자호전2례,여환자증상무명현개변.제일차수방MRI검사현시척수공동소실5례、축소4례、무변화3례,무일례척수공동확대,3례합병뇌적수자뇌실명현축소.제이차수방MRI검사여제일차수방상비무명현변화.결론 소뇌편도체하산연뇌막하절제병주망막수보침대지중건개량수술대Arnold-Chiari기형Ⅰ형합병척수공동치료구유량호효과.
Objective To evaluate the methods and effects of modified surgical treatment for Amold-Chiari Ⅰ malformation complicated with syringomyelia.Methods Twelve patients with ArnoldChiari Ⅰ malformation complicated with syringomyelia,underwent a modified surgical treatment,effects were observed.Results During the first follow-up,sensation and motion function were significantly improved in 10 cases,unchanged in 2 cases.During the second follow-up,2 cases previously unchanged were improved,while the other were with no change.During the first follow-up,lesion showed on MRI disappeared in 5 cases,reduced in 4 cases,no significant change in 3 cases,no case extend,3 cases with hydrocephalus ventricle was significantly reduced.The second follow-up,MRI showed that there was no change compared with the first follow-up.Conclusion The remove of the pia mater of tonsillar hernia + reconstruction the cisterna magna have good effect on surgical therapies for Arnold-Chiari I malformation complicated with syringomyelia.