CAJ | 학술논문

肝窦阻塞综合征(HSOS)是一种肝窦或是小静脉纤维性闭塞的疾病,其主要临床特征为肝脏肿大,高胆红素血症,腹水,体重快速增长等.目前,HSOS发病率不断增加,但发病机制尚不清楚,治疗手段有限.为提高对该病的认识,此文就其病因、发病机制、诊断和治疗情况作一综述.
간두조새종합정(HSOS)시일충간두혹시소정맥섬유성폐새적질병,기주요림상특정위간장종대,고담홍소혈증,복수,체중쾌속증장등.목전,HSOS발병솔불단증가,단발병궤제상불청초,치료수단유한.위제고대해병적인식,차문취기병인、발병궤제、진단화치료정황작일종술.
Hepatic sinusoidal obstruction syndrome(HSOS) is a kind of sinusoid or small venous fibrous occlusive disease,with the clinical features of hepatomegaly,hyperbilirubinemia,ascites and rapid weight gain.Currently,HSOS incidence is increasing,while the pathogenesis is unclear and the treatment is limited.To deepen the understanding of this disease,the aetiology,pathology,diagnosis and treatment of HSOS are summarized in this article.