CAJ | 학술논문

目的：分析心脏乳头状弹力纤维瘤的临床病理学特征，为临床诊疗及判断预后提供依据。方法对我院10年间收治的6例心脏乳头状纤维瘤进行HE染色及弹力纤维EVG染色，回顾性分析其临床资料及病理学特征。结果肿瘤典型外观呈“海葵样”。镜下呈分支细乳头状，表面被覆一层内皮细胞。弹力纤维染色可见较多弹力纤维。术后随访3个月～8年，6例患者均恢复情况良好，无复发。结论心脏乳头状弹力纤维瘤非常罕见，为心脏原发性良性肿瘤，好发于心脏瓣膜上；其临床症状缺乏特异性，临床诊断困难，但其组织形态学的特征典型，病理学检查易诊断。
목적：분석심장유두상탄력섬유류적림상병이학특정，위림상진료급판단예후제공의거。방법대아원10년간수치적6례심장유두상섬유류진행HE염색급탄력섬유EVG염색，회고성분석기림상자료급병이학특정。결과종류전형외관정“해규양”。경하정분지세유두상，표면피복일층내피세포。탄력섬유염색가견교다탄력섬유。술후수방3개월～8년，6례환자균회복정황량호，무복발。결론심장유두상탄력섬유류비상한견，위심장원발성량성종류，호발우심장판막상；기림상증상결핍특이성，림상진단곤난，단기조직형태학적특정전형，병이학검사역진단。
Objective To study the clinical and pathological characteristics of cardiac papillary fibroelastoma which could fa-cilitate the diagnosis and treatment. Methods Six cases of cardiac papillary fibroelastoma which were treated in our hospital in the re-cent 10 years were reviewed retrospectively. All the cases of cardiac papillary fibroelastoma were stained routinely by HE and an elastic stain. Results The typical tumor showed the appearance of sea anemone. It was coated by a layer of endothelial cells, and fine papil-lary branches can be observed under a microscope. There were some elastic fibers in the tumor. The patients were followed for 3 months to 8 years, and no recurrence was observed. Conclusion Cardiac papillary fibroelastomas is rare, and it is a primary benign tumor of the heart valves. The clinical manifestations of cardiac papillary fibroelastoma are not characteristic, it is hard to diagnose according to clinical manifestations. But the tumor has typical histomorphological features, it can be diagnosed by pathological examination.