CAJ | 학술논문

目的：探讨原发性骨上皮样血管肉瘤的影像特点，以提高其影像诊断水平。方法回顾性分析6例经病理证实原发性骨上皮样血管肉瘤的影像学表现。其中男2例，女4例，中位年龄51．7岁，病程1～12个月。结果6例原发性骨上皮样血管肉瘤患者均行影像学检查，其中单独行X线平片检查1例，X线平片＋CT 1例，X线平片＋MR 2例，X线平片＋CT＋MR 2例。 X线平片及CT表现：5例为单发病灶，1例为多中心发病；5例呈斑片状、地图样的溶骨性骨质破坏，呈轻度膨胀，无硬化边、钙化及骨膜反应；1例呈皂泡状明显膨胀生长，可见基本完整的硬化边，瘤内可见不规则钙化影。 MR表现：肿瘤呈等T1、长T2信号影，增强扫描肿瘤呈明显不均匀强化，呈等、稍高或低T1WI信号，T2WI高信号，1例瘤内可见小片状长T1、T2区。结论原发性骨上皮样血管肉瘤是一种以肿瘤性内皮细胞呈上皮样形态为其特征的高度恶性血管源性肿瘤，影像表现缺乏特征性，确诊依靠病理检查。
목적：탐토원발성골상피양혈관육류적영상특점，이제고기영상진단수평。방법회고성분석6례경병리증실원발성골상피양혈관육류적영상학표현。기중남2례，녀4례，중위년령51．7세，병정1～12개월。결과6례원발성골상피양혈관육류환자균행영상학검사，기중단독행X선평편검사1례，X선평편＋CT 1례，X선평편＋MR 2례，X선평편＋CT＋MR 2례。 X선평편급CT표현：5례위단발병조，1례위다중심발병；5례정반편상、지도양적용골성골질파배，정경도팽창，무경화변、개화급골막반응；1례정조포상명현팽창생장，가견기본완정적경화변，류내가견불규칙개화영。 MR표현：종류정등T1、장T2신호영，증강소묘종류정명현불균균강화，정등、초고혹저T1WI신호，T2WI고신호，1례류내가견소편상장T1、T2구。결론원발성골상피양혈관육류시일충이종류성내피세포정상피양형태위기특정적고도악성혈관원성종류，영상표현결핍특정성，학진의고병리검사。
Objective To study the imaging features of primary bone epithelioid angiosarcoma , to improve the diag-nostic accuracy .Methods Retrospective analysis of 6 cases confirmed by pathology image of primary bone epithelioid angio-sarcoma manifestations.There were 2 male, 4 female, median age 51.7 years, the course of 1-12 months.Results 6 cases of primary bone epithelioid angiosarcoma patients underwent imaging examination , including 1 cases only underwent X-ray ex-amination, X-ray plain film +CT of 1 cases, 2 cases of X-ray plain film+MR, 2 cases of X-ray plain film +CT+MR.The X-ray and CT manifestations:5 cases were with single lesion , 1 cases of multi center for disease;5 cases showed patchy , map like osteolytic bone destruction , a mild swelling, no sclerosis, calcification and periosteal reaction;1 cases were soap bubble obvious expansion growth , hardening visible the basic integrity of the edge , tumor shows irregular calcification .MR features:the tumor was iso-T1, long T2 signal intensity, enhancement of tumor showed inhomogeneous enhancement , with slightly high or low signal in T1WI, high signal on T2WI, 1 cases of tumor can be seen in the small pieces of long T 1, T2 area.Conclu-sion Primary bone epithelioid angiosarcoma is a kind of tumor that endothelial cells were epithelioid morphology as characte -rized and highly malignant vascular tumors , imaging showed lack of characteristic , diagnosis depends on pathological examina-tion.