罕少疾病杂志
罕少疾病雜誌
한소질병잡지
JOURNAL OF RARE AND UNCOMMON DISEASES
2014年
4期
42-44
,共3页
罗津%董金凯%李钢%高江平%谢皓空
囉津%董金凱%李鋼%高江平%謝皓空
라진%동금개%리강%고강평%사호공
肾肿瘤%多房性囊性肾瘤
腎腫瘤%多房性囊性腎瘤
신종류%다방성낭성신류
Kidney Neoplasm%Multilocular Cystic Nephroma
目的:回顾性分析9例MCN患者的临床资料并结合文献讨论MCN的临床表现、病理学特征、诊断和治疗方法。方法男性5例,年龄12-85岁,平均53.3岁;女性4例,年龄32-71岁,平均56.4岁。临床表现为肉眼血尿1例,腹部包块2例,腹痛2例,无症状体检发现4例。所有肿块均为单发,大小2.5cm×3.0cm-12.0cm×6.5cm。所有病例均行B超、IVU和增强CT检查。结果 B超诊断MCN1例、囊性肾癌3例、肾囊肿5例;CT诊断MCN2例、囊性肾癌4例、未定性3例;IVU均未定性。行肾脏切除术2例,肾肿瘤剜除术5例,肾根治性切除术2例。术后病理诊断均为MCN。随访3-36个月均未见复发且患者患侧未见肾功能障碍。结论影像学检查是MCN的重要检查手段,保留肾单位的肿瘤切除术是本病的首选治疗方法。
目的:迴顧性分析9例MCN患者的臨床資料併結閤文獻討論MCN的臨床錶現、病理學特徵、診斷和治療方法。方法男性5例,年齡12-85歲,平均53.3歲;女性4例,年齡32-71歲,平均56.4歲。臨床錶現為肉眼血尿1例,腹部包塊2例,腹痛2例,無癥狀體檢髮現4例。所有腫塊均為單髮,大小2.5cm×3.0cm-12.0cm×6.5cm。所有病例均行B超、IVU和增彊CT檢查。結果 B超診斷MCN1例、囊性腎癌3例、腎囊腫5例;CT診斷MCN2例、囊性腎癌4例、未定性3例;IVU均未定性。行腎髒切除術2例,腎腫瘤剜除術5例,腎根治性切除術2例。術後病理診斷均為MCN。隨訪3-36箇月均未見複髮且患者患側未見腎功能障礙。結論影像學檢查是MCN的重要檢查手段,保留腎單位的腫瘤切除術是本病的首選治療方法。
목적:회고성분석9례MCN환자적림상자료병결합문헌토론MCN적림상표현、병이학특정、진단화치료방법。방법남성5례,년령12-85세,평균53.3세;녀성4례,년령32-71세,평균56.4세。림상표현위육안혈뇨1례,복부포괴2례,복통2례,무증상체검발현4례。소유종괴균위단발,대소2.5cm×3.0cm-12.0cm×6.5cm。소유병례균행B초、IVU화증강CT검사。결과 B초진단MCN1례、낭성신암3례、신낭종5례;CT진단MCN2례、낭성신암4례、미정성3례;IVU균미정성。행신장절제술2례,신종류완제술5례,신근치성절제술2례。술후병리진단균위MCN。수방3-36개월균미견복발차환자환측미견신공능장애。결론영상학검사시MCN적중요검사수단,보류신단위적종류절제술시본병적수선치료방법。
Objective To retrospectively analyze the clinical data of 9 case with multilocalar cystic nephroma and review related literatures, and to discuss the clinical features, pathological manifestations,diagnosis and treatment methods. Methods The clinical data of 9 cases (5 males, 12 to 85 years old; 4 female, 32 to 71 years old) of MCN were retrospectively analyzed; Among the 9 cases, 1 showed macroscopic hematuria and 2 showed abdominal masses; 2 showed abdominal pain,and other 4 cases showed no symptoms and the tumors were found accidentally during physical examination. The tumors were all solitary and showed 2.5cm×3.0cm to 12.0cm×6.5cm in size. Ultrasound examination, IVU and enhanced CT scanning were performed in all cases.Results On ultrasound examination, 1 case was diagnosed with MCN, 5 cases were diagnosed with renal cyst and 3 with cystic renal carcinoma. On CT, 2 cases were diagnosed with MCN, 4 cases with cystic renal carcinoma and 3 cases with uncertain diagnosis. On IVU, the diagnosis was not established in all cases. 4 cases underwent nephrectomy and 5 cases underwent enucleation of the tumors with nephronsparing surgery. Postoperative pathology showed MCN in all cases. During the follow-up of 3-36 months, the patients were well with no evidence of recurrence and renal dysfunction. Conclusions Imaging examinations are important to the detection of MCN, and nephronsparing resection of tumor is a primary and effective therapeutic method for this disease.