罕少疾病杂志
罕少疾病雜誌
한소질병잡지
JOURNAL OF RARE AND UNCOMMON DISEASES
2014年
4期
12-15
,共4页
游勇%胡元明%李春生%吕涵青%王立振%段柯
遊勇%鬍元明%李春生%呂涵青%王立振%段柯
유용%호원명%리춘생%려함청%왕립진%단가
肝脏%血管平滑肌脂肪瘤%体层摄影术%X线计算机
肝髒%血管平滑肌脂肪瘤%體層攝影術%X線計算機
간장%혈관평활기지방류%체층섭영술%X선계산궤
Hepatic%Angiomyolipoma%Computed Tomography
目的:探讨肝脏血管平滑肌脂肪瘤(HAML)的CT表现特征以提高术前确诊率。方法回顾性分析12例经病理证实为HAML的临床、病理和CT表现特征。记录病灶部位、大小、边缘、密度、血运和强化特征。结果 HAML病灶表现为边界清楚、孤立性的肿块。12例患者中,8例病灶中可见脂肪,1例伴有钙化,1例可见囊性变;动脉期CT值超过120Hu 11例(91.7%);出现外周强化逐渐降低和动脉期肝静脉早显的患者均为10例(83.3%);未见肝硬化和逐渐强化的假包膜。结论 CT上表现为富血供、动脉期肝静脉早期显影、外周强化逐渐降低,无假包膜是HAML与肝癌的重要鉴别点。
目的:探討肝髒血管平滑肌脂肪瘤(HAML)的CT錶現特徵以提高術前確診率。方法迴顧性分析12例經病理證實為HAML的臨床、病理和CT錶現特徵。記錄病竈部位、大小、邊緣、密度、血運和彊化特徵。結果 HAML病竈錶現為邊界清楚、孤立性的腫塊。12例患者中,8例病竈中可見脂肪,1例伴有鈣化,1例可見囊性變;動脈期CT值超過120Hu 11例(91.7%);齣現外週彊化逐漸降低和動脈期肝靜脈早顯的患者均為10例(83.3%);未見肝硬化和逐漸彊化的假包膜。結論 CT上錶現為富血供、動脈期肝靜脈早期顯影、外週彊化逐漸降低,無假包膜是HAML與肝癌的重要鑒彆點。
목적:탐토간장혈관평활기지방류(HAML)적CT표현특정이제고술전학진솔。방법회고성분석12례경병리증실위HAML적림상、병리화CT표현특정。기록병조부위、대소、변연、밀도、혈운화강화특정。결과 HAML병조표현위변계청초、고립성적종괴。12례환자중,8례병조중가견지방,1례반유개화,1례가견낭성변;동맥기CT치초과120Hu 11례(91.7%);출현외주강화축점강저화동맥기간정맥조현적환자균위10례(83.3%);미견간경화화축점강화적가포막。결론 CT상표현위부혈공、동맥기간정맥조기현영、외주강화축점강저,무가포막시HAML여간암적중요감별점。
Objective To evaluate the computed tomography (CT) findings of hepatic angiomyolipoma (HAML) and to improve the diagnostic efficacy of the tumor. Methods Clinical characteristics, pathology, and CT imaging findings were retrospectively evaluated in 12 patients with HAML. All the patients underwent CT with unenhanced and contrast-enhanced examinations. Imaging characteristics, such as the lesion location, lesion diameter, presence of early draining veins and enhancement pattern were reviewed. Results HAML was seen as a well-defined, solitary mass on CT imaging. Fat was detected in eight patients. Calcification was noted in one patients and cystic degeneration was seen in one patient. The mean attenuation values exceeded 120 hounsfield units (Hu) in 11 patients (91.7%). Peripherally decreasing enhancement rim or early draining vein was seen in 10 patients (83.3%). The early draining veins were all hepatic veins. Hepatic cirrhosis and capsule were not detected in all patients. Conclusion The presence of early draining vein, peripheral decreasing enhancement rim, and the absence of tumor capsule may be helpful for the diagnosis of HAML.