CAJ | 학술논문

目的：回顾性分析 Sturge-Weber 综合征在小于1岁婴儿中的颅脑 MRI 表现及其临床诊断价值。方法：回顾性分析7例小于1岁的 Sturge-Weber 综合征患儿的 MRI 图像，7例行 MRI 平扫，6例行 MRI 增强扫描。结果：本组患儿均有面部三叉神经分布区的血管瘤。5例病变累及单侧大脑半球，均可见病变区脑白质于 T2 WI 上信号明显减低，伴有局部脑萎缩改变，其中4例可见患侧脉络丛扩大；2例累及双侧大脑半球脑叶。6例增强后均可见脑回表面软脑膜强化，其中5例可见异常强化的软脑膜血管瘤，1例同时见幕下结构受累。结论：对临床怀疑为 Sturge-Weber 综合征的婴儿，MRI增强扫描可以帮助明确诊断及确定病变范围，为临床评估患儿的预后提供有效的参考信息。
목적：회고성분석 Sturge-Weber 종합정재소우1세영인중적로뇌 MRI 표현급기림상진단개치。방법：회고성분석7례소우1세적 Sturge-Weber 종합정환인적 MRI 도상，7례행 MRI 평소，6례행 MRI 증강소묘。결과：본조환인균유면부삼차신경분포구적혈관류。5례병변루급단측대뇌반구，균가견병변구뇌백질우 T2 WI 상신호명현감저，반유국부뇌위축개변，기중4례가견환측맥락총확대；2례루급쌍측대뇌반구뇌협。6례증강후균가견뇌회표면연뇌막강화，기중5례가견이상강화적연뇌막혈관류，1례동시견막하결구수루。결론：대림상부의위 Sturge-Weber 종합정적영인，MRI증강소묘가이방조명학진단급학정병변범위，위림상평고환인적예후제공유효적삼고신식。
Objective:Retrospective study of cerebral MR imaging features of Sturge-Weber syndrome (SWS)in in-fant less than 1y of age was performed,and their clinical significance was evaluated.Methods:The MRI features of 7 infants less than 1y age with SWS were retrospectively analyzed.All had plain MRI,6 patients had enhanced MRI.Results:All pa-tients had characteristic features of angioma involving facial-trigerminal nerves distributed area.Unilateral cerebral sphere was involved in 5 patients,the signal intensities of involved white matters on T2 WI were significantly reduced,accompanied with local brain atrophy and and choroid plexus enlargement (n=4);2 patients had bilateral cerebral spheres involved.In the 6 infants with contrast-enhanced MRI,letomeningeal enhancement could be revealed,5 patients had marked enhanced leptomeningeal angioma,1 patient had infratentorial structures involvement simultaneously.Conclusion:For infants with clinically suspected SWS,contrast enhanced MRI is helpful in the diagnosis and demonstration of involved regions,provides significant reference for the prognosis.