国际呼吸杂志
國際呼吸雜誌
국제호흡잡지
INTERNATIONAL JOURNAL OF RESPIRATION
2014年
15期
1179-1181
,共3页
代宜凝%夏书月%赵龙%鲁钢%刘放
代宜凝%夏書月%趙龍%魯鋼%劉放
대의응%하서월%조룡%로강%류방
普通变异型免疫缺陷病%支气管扩张
普通變異型免疫缺陷病%支氣管擴張
보통변이형면역결함병%지기관확장
Common variable immunodefieiency%Bronchiectasis
目的:提高对普通变异型免疫缺陷病的认识。方法报道1例普通变异型免疫缺陷病合并支气管扩张病例并进行相关文献复习。结果结合患者症状体征及相关辅助检查,明确诊断为普通变异型免疫缺陷病合并支气管扩张,给予相应治疗后症状好转。结论普通变异型免疫缺陷病起病较晚,且临床表现多样,易与其他疾病混淆而误诊,早期诊断及规范治疗可以改善预后。
目的:提高對普通變異型免疫缺陷病的認識。方法報道1例普通變異型免疫缺陷病閤併支氣管擴張病例併進行相關文獻複習。結果結閤患者癥狀體徵及相關輔助檢查,明確診斷為普通變異型免疫缺陷病閤併支氣管擴張,給予相應治療後癥狀好轉。結論普通變異型免疫缺陷病起病較晚,且臨床錶現多樣,易與其他疾病混淆而誤診,早期診斷及規範治療可以改善預後。
목적:제고대보통변이형면역결함병적인식。방법보도1례보통변이형면역결함병합병지기관확장병례병진행상관문헌복습。결과결합환자증상체정급상관보조검사,명학진단위보통변이형면역결함병합병지기관확장,급여상응치료후증상호전。결론보통변이형면역결함병기병교만,차림상표현다양,역여기타질병혼효이오진,조기진단급규범치료가이개선예후。
Objective To promote the awareness of common variable immunodefiency (CVID). Methods Report one cases of CVID complicated with bronchiectasis and review related literature.Results According to symptom,sign and accessory examination we can definitely diagnose CVID complicated with bronchiectasis.The patient was treated with intravenous gammaglobulin,anti-infection and the disease were well controlled.Conclusions CVID is a disease with later-onset,characterized by a variety of clinical manifestations.Physicians are prone to confused it with other diseases.Early diagnosis and regular treatment can improve the prognosis.