CAJ | 학술논문

指状突树突细胞肉瘤（IDCS）是一种极罕见的造血组织来源的树突细胞恶性肿瘤，主要表现为浅表淋巴结肿大，也可以发生于肺脏、肾脏、膀胱、胸膜等不典型的部位。随着病理诊断水平提高、免疫组织化学及电镜的应用，该病诊断检出率明显升高。目前手术仍是该病治疗的主要手段，但由于疾病恶性程度高、进展迅速，具有不良的预后。
지상돌수돌세포육류（IDCS）시일충겁한견적조혈조직래원적수돌세포악성종류，주요표현위천표림파결종대，야가이발생우폐장、신장、방광、흉막등불전형적부위。수착병리진단수평제고、면역조직화학급전경적응용，해병진단검출솔명현승고。목전수술잉시해병치료적주요수단，단유우질병악성정도고、진전신속，구유불량적예후。
Interdigitating dendritic cell sarcoma (IDCS)is a rare malignant tumor of the dendritic cell, derived from the hematopoietic tissue.The major clinical manifestation of IDCS is superficial lymphadenopathy, and the enlarged lymph nodes may appear in some atypical ereas,such as the lung,kidney,bladder and the pleura,etc.With the development of the pathological diagnosis and the application of immunohistochemical staining and electron microscopes,the case detection rate is apparently improved.With the high degree of malignant,rapid progress and poor prognosis of the disease,currently,surgical therapy is still the main approach to the treatment of IDCS.