国际呼吸杂志
國際呼吸雜誌
국제호흡잡지
INTERNATIONAL JOURNAL OF RESPIRATION
2014年
10期
753-756
,共4页
肺朗格汉斯组织细胞增生症%诊断%治疗%文献复习
肺朗格漢斯組織細胞增生癥%診斷%治療%文獻複習
폐랑격한사조직세포증생증%진단%치료%문헌복습
Pulmonary Langerhans cell histiocytosis%Diagnosis%Treatment%Literature analysis
目的 提高对朗格汉斯组织细胞增生症的认识.方法 回顾性分析我院病理确诊的1例复发性成人肺朗格汉斯组织细胞增生症的临床资料,并进行相关文献分析,对肺朗格汉斯组织细胞增生症的临床表现及其诊治进行讨论.结果 朗格汉斯组织细胞增生症是一种病因不详、临床极易误诊、可累及全身各个系统的少见病,依靠典型的临床表现和病理学检查可诊断,治疗手段包括手术、化疗、放射及激素治疗.结论 典型临床病例结合文献分析,增加临床医师对肺朗格汉斯组织细胞增生症的了解,可提高早期诊治肺朗格汉斯组织细胞增生症的能力.
目的 提高對朗格漢斯組織細胞增生癥的認識.方法 迴顧性分析我院病理確診的1例複髮性成人肺朗格漢斯組織細胞增生癥的臨床資料,併進行相關文獻分析,對肺朗格漢斯組織細胞增生癥的臨床錶現及其診治進行討論.結果 朗格漢斯組織細胞增生癥是一種病因不詳、臨床極易誤診、可纍及全身各箇繫統的少見病,依靠典型的臨床錶現和病理學檢查可診斷,治療手段包括手術、化療、放射及激素治療.結論 典型臨床病例結閤文獻分析,增加臨床醫師對肺朗格漢斯組織細胞增生癥的瞭解,可提高早期診治肺朗格漢斯組織細胞增生癥的能力.
목적 제고대랑격한사조직세포증생증적인식.방법 회고성분석아원병리학진적1례복발성성인폐랑격한사조직세포증생증적림상자료,병진행상관문헌분석,대폐랑격한사조직세포증생증적림상표현급기진치진행토론.결과 랑격한사조직세포증생증시일충병인불상、림상겁역오진、가루급전신각개계통적소견병,의고전형적림상표현화병이학검사가진단,치료수단포괄수술、화료、방사급격소치료.결론 전형림상병례결합문헌분석,증가림상의사대폐랑격한사조직세포증생증적료해,가제고조기진치폐랑격한사조직세포증생증적능력.
Objective To improve the understanding of adult recurrent pulmonary Langerhans cell histiocytosis (PLCH).Methods One case of adult recurrent PLCH was retrospectively analyzed,and the literatures related to this disease were searched to summarize and analyze the clinical manifestations,diagnosis and treatment of this disease.Results Langerhans cell histiocytosis (LCH) is a rare and stubborn disease with scarcely active treatment till now.The diagnosis of LCH is based on histological and immunophenotypic examination of lesional tissue.The main feature is the morphologic identification of the characteristic LCH cells.The treatment of LCH included operation,chemotherapy,radiotherapy,and hormone therapy.Conclusions Typical clinical case combined with literature analysis could improve the effect of diagnosis and treatment of PLCH.