国际免疫学杂志
國際免疫學雜誌
국제면역학잡지
INTERNATIONAL JOURNAL OF IMMUNOLOGY
2014年
2期
133-136
,共4页
惠普尔病%惠普尔养障体
惠普爾病%惠普爾養障體
혜보이병%혜보이양장체
Whipple's Disease%Tropheryma Whipplei
惠普尔病(WD)是由惠普尔养障体引起的可累及多系统病变的慢性感染性疾病.WD的临床表现多样且无特征性,临床上常被误诊.惠普尔养障体在环境中广泛存在而WD患者却很少见,最近的研究提示,机体的某些免疫病理因素可能在WD的发病机制中起重要作用.了解惠普尔病及其病原体的流行病学、免疫致病机制、临床表现及实验室诊断和治疗等方面的研究进展很重要.
惠普爾病(WD)是由惠普爾養障體引起的可纍及多繫統病變的慢性感染性疾病.WD的臨床錶現多樣且無特徵性,臨床上常被誤診.惠普爾養障體在環境中廣汎存在而WD患者卻很少見,最近的研究提示,機體的某些免疫病理因素可能在WD的髮病機製中起重要作用.瞭解惠普爾病及其病原體的流行病學、免疫緻病機製、臨床錶現及實驗室診斷和治療等方麵的研究進展很重要.
혜보이병(WD)시유혜보이양장체인기적가루급다계통병변적만성감염성질병.WD적림상표현다양차무특정성,림상상상피오진.혜보이양장체재배경중엄범존재이WD환자각흔소견,최근적연구제시,궤체적모사면역병리인소가능재WD적발병궤제중기중요작용.료해혜보이병급기병원체적류행병학、면역치병궤제、림상표현급실험실진단화치료등방면적연구진전흔중요.
The patients with Whipple's disease(WD) may appear numerous nonspecific symptoms,so they are often misdiagnosed.Tropheryma Whipplei is a ubiquitous commensal bacterium in the environment,but the cases of WD are very rare.Recent studies have shown that some undefined predisposing immune pathologic factors might play a role in the pathogenesis.This paper reviews the research progress of WD and it' s pathogen in epidemiology,immunopathology,clinical manifestations,laboratory diagnosis and the treatment of the disease.