国际眼科纵览
國際眼科縱覽
국제안과종람
OREIGN MEDICAL SCIENCES
2013年
5期
303-307
,共5页
柯梅青%张兴儒%赵黎%韩竹梅%李青松
柯梅青%張興儒%趙黎%韓竹梅%李青鬆
가매청%장흥유%조려%한죽매%리청송
眼睑皮肤松弛综合征%眼睑疾病%临床表现%发病机制%治疗
眼瞼皮膚鬆弛綜閤徵%眼瞼疾病%臨床錶現%髮病機製%治療
안검피부송이종합정%안검질병%림상표현%발병궤제%치료
blepharochalasis syndrome%eyelid disease%clinical manifestation%pathogenesis%therapy
眼睑皮肤松弛综合征是一种较少见的眼睑疾病,表现为青少年时期特发性局限性眼睑皮肤反复间断性无痛性血管神经性水肿,反复水肿破坏眼睑组织结构导致眼睑皮肤松弛变薄,毛细血管增多迂曲扩张以及后期上睑下垂、眶脂肪脱垂、泪腺脱垂等多种并发症.眼睑皮肤松弛综合征的发病机制尚不明确,可能存在遗传等因素的参与;组织病理学研究发现IgA沉积和基质金属蛋白酶活性表达增强,提示免疫反应参与弹性纤维的降解,后者进一步引起局部淋巴系统结构功能的改变;这些因素共同参与了本病的发生发展.眼睑皮肤松弛综合征的治疗分为急性水肿期和稳定期的治疗.
眼瞼皮膚鬆弛綜閤徵是一種較少見的眼瞼疾病,錶現為青少年時期特髮性跼限性眼瞼皮膚反複間斷性無痛性血管神經性水腫,反複水腫破壞眼瞼組織結構導緻眼瞼皮膚鬆弛變薄,毛細血管增多迂麯擴張以及後期上瞼下垂、眶脂肪脫垂、淚腺脫垂等多種併髮癥.眼瞼皮膚鬆弛綜閤徵的髮病機製尚不明確,可能存在遺傳等因素的參與;組織病理學研究髮現IgA沉積和基質金屬蛋白酶活性錶達增彊,提示免疫反應參與彈性纖維的降解,後者進一步引起跼部淋巴繫統結構功能的改變;這些因素共同參與瞭本病的髮生髮展.眼瞼皮膚鬆弛綜閤徵的治療分為急性水腫期和穩定期的治療.
안검피부송이종합정시일충교소견적안검질병,표현위청소년시기특발성국한성안검피부반복간단성무통성혈관신경성수종,반복수종파배안검조직결구도치안검피부송이변박,모세혈관증다우곡확장이급후기상검하수、광지방탈수、루선탈수등다충병발증.안검피부송이종합정적발병궤제상불명학,가능존재유전등인소적삼여;조직병이학연구발현IgA침적화기질금속단백매활성표체증강,제시면역반응삼여탄성섬유적강해,후자진일보인기국부림파계통결구공능적개변;저사인소공동삼여료본병적발생발전.안검피부송이종합정적치료분위급성수종기화은정기적치료.
Blepharochalasis syndrome is a rare eyelid disease that often presents in childhood or adolescence.It is characterized by idiopathic localized intermittent painless edema of upper and(or) lower eyelids,which would destroy the tissue structure of eyelid and lead to atrophic,wrinkled periorbital skin and the tortuous and dilated capillaries.Other clinical manifestations include proptosis,prolapse of orbital fat,and lacrimal tissue,etc.The etiology of the blepharochalasis syndrome has not yet to be fully elucidated.It still cannot exclude the participation of genetic factors.IgA and matrix metalloproteinases had been found in the periorbital tissues,which confirm that participation of the immuoreaction which might lead to elastolysis.Elastolysis may ruin the structure and the function of the lymphatic system.All these factors may play a substantial role in the pathogenesis of the disease.The treatment of blepharochalasis divided into the treatment of acute edema and stable period.