CAJ | 학술논문

先天性纯红细胞再生障碍性贫血是临床上罕见的红细胞发育不良性疾病.因缺乏此种疾病完整的自然演变信息,对其诊断、治疗及预后评估尚无统一认识,尤其在国内,更缺乏对该病系统的认识.该文主要综述该病的诊断标准,评价可行性治疗方法,包括激素等药物治疗及输血和造血干细胞移植等.
선천성순홍세포재생장애성빈혈시림상상한견적홍세포발육불량성질병.인결핍차충질병완정적자연연변신식,대기진단、치료급예후평고상무통일인식,우기재국내,경결핍대해병계통적인식.해문주요종술해병적진단표준,평개가행성치료방법,포괄격소등약물치료급수혈화조혈간세포이식등.
Diamond-Blackfan anemia(DBA)is a rare disease with depauperate red blood cells.For absence of its whole naturally successive information,it is very hard to know distinctly its diagnositic and curative viewpoints to evaluate its prognosis.Especially domestically,its systematic study is more insufficient.The paper approaches its diagnostic criteria and evaluates its feasibly curative viewpoints,including hormone drugs treatment,blood-transfusion treatment and transplanting haemopoietic stem cells.