CAJ | 학술논문

视网膜和视网膜色素上皮联合错构瘤(combined hamartoma of the retina and retinal pigment epithelium,CHRRPE)是一种少见的眼部良性肿瘤,可累及视盘、黄斑或周边视网膜,常见于儿童,其临床特征为瘤体位于视网膜,隆起,有不同程度的色素增生、血管迂曲及视网膜前膜形成.组织病理学检查显示CHRRPE主要由杂乱的胶质、视网膜血管及增生的视网膜色素上皮细胞构成.相干光断层扫描有助于本病的诊断,并可指导治疗.玻璃体切除联合视网膜前膜剥除术可在一定程度上恢复患眼的视网膜结构,稳定或提高视力.(
시망막화시망막색소상피연합착구류(combined hamartoma of the retina and retinal pigment epithelium,CHRRPE)시일충소견적안부량성종류,가루급시반、황반혹주변시망막,상견우인동,기림상특정위류체위우시망막,륭기,유불동정도적색소증생、혈관우곡급시망막전막형성.조직병이학검사현시CHRRPE주요유잡란적효질、시망막혈관급증생적시망막색소상피세포구성.상간광단층소묘유조우본병적진단,병가지도치료.파리체절제연합시망막전막박제술가재일정정도상회복환안적시망막결구,은정혹제고시력.(
Combined hamartoma of the retina and retinal pigment epithelium (CHRRPE) is a rare benign lesion in the macula,parapapillary,or peripheral retina that is commonly found in children.Clinical characteristics were elevation in retina,diferent degree of hyperpigmentation,retinal vascular tortuosity,as well as epiretinal membrane formation.Histopathologically,CHRRPE consists of disorganized glial tissue intermixed with numerous blood vessels and proliferating retinal pigment epithelium cells.Optical coherence tomography is a helpful tool in the diagnosis and management of CHRRPE.Pars plana vitrectomy with membrane peeling may result in restored retinal architecture to some extent and improved or stabled visual acuity for patients with CHRRPE.