CAJ | 학술논문

目的探讨胎儿右室双出口(double outlet of right ventricle,DORV)的超声诊断、病理解剖分型和预后.方法采用系统多切面胎儿超声心动图检查方法,分析经我院筛查并确诊的59例胎儿DORV的超声表现特点、病理解剖分型与合并畸形.结果 59例DORV中56例心房与心室连接一致;主动脉右转位44例,左转位7例,大血管关系正常2例,早期未分类6例;53例DORV中SDD型最常见,约占81％ (43/53);合并畸形包括肺动脉口狭窄21例,单心房5例,房室瓣狭窄3例,升主动脉发育较细2例.羊水穿刺染色体检查7例,其中5例染色体正常,21-三体及18-三体各1例.结论胎儿超声心动图能够准确诊断胎儿DORV,判断其分型,检测合并畸形,详细的检查能够评估出生后的手术方式和预后.
목적 탐토태인우실쌍출구(double outlet of right ventricle,DORV)적초성진단、병리해부분형화예후.방법 채용계통다절면태인초성심동도검사방법,분석경아원사사병학진적59례태인DORV적초성표현특점、병리해부분형여합병기형.결과 59례DORV중56례심방여심실련접일치;주동맥우전위44례,좌전위7례,대혈관관계정상2례,조기미분류6례;53례DORV중SDD형최상견,약점81％ (43/53);합병기형포괄폐동맥구협착21례,단심방5례,방실판협착3례,승주동맥발육교세2례.양수천자염색체검사7례,기중5례염색체정상,21-삼체급18-삼체각1례.결론 태인초성심동도능구준학진단태인DORV,판단기분형,검측합병기형,상세적검사능구평고출생후적수술방식화예후.
Objective To study the accuracy of diagnosis,anatomical classification and prognostic prediction of double outlet of right ventricle (DORV) by fetal echocardiography.Methods Fifty-nine fetuses detected and diagnosed with DORV by fetal echocardiography were investigated to analyze the anatomical characteristics,types and complicated malformations.Results Fifty-nine fetuses with DORV included 56 with atrioventricular accordance and 3 with atrioventricular discordance.Among them,there were 44 with dextro-transposition of great arteries,7 with levo-transposition,2 with normal position,6 with un-identified in early stage.SDD was the most common type in DORV for approximate 81％ (44/53).Complicated abnormalities included pulmonary artery stenosis in 21 fetuses,single atrium in 5,atrialventricular valvular stenosis in 3,and mild ascending aortic dysplasia in 2.Amniocentesis and chromosome were test in 7 fetuses including 5 fetuses with normal chromosomes,one with trisomy 21 and one with trisomy 18.Conclusions Fetal echocardiography shows high clinical value in diagnosis,classification and detecting complicated abnormalities of DORV.Careful examinations provide accurate evaluation in surgical procedure and prognosis.