中华实用儿科临床杂志
中華實用兒科臨床雜誌
중화실용인과림상잡지
Journal of Applied Clinical Pediatrics
2014年
23期
1763-1768
,共6页
先天性巨结肠%巨结肠同源病%节细胞减少症%肠神经元发育不良症
先天性巨結腸%巨結腸同源病%節細胞減少癥%腸神經元髮育不良癥
선천성거결장%거결장동원병%절세포감소증%장신경원발육불량증
Hirschsprung's disease%Hirschsprung's disease allied disorders%Hypoganglionosis%Intestinal neuronal dysplasia
肠道神经系统病变是慢性小儿便秘的重要原因,这些病变包括先天性巨结肠,也包括巨结肠同源病,如节细胞不成熟、节细胞减少症及肠神经元发育不良症等.目前对同源病的病因、诊断及治疗方式尚有广泛的争议和不确定性,现对巨结肠同源病的诊断和治疗相关问题介绍如下.
腸道神經繫統病變是慢性小兒便祕的重要原因,這些病變包括先天性巨結腸,也包括巨結腸同源病,如節細胞不成熟、節細胞減少癥及腸神經元髮育不良癥等.目前對同源病的病因、診斷及治療方式尚有廣汎的爭議和不確定性,現對巨結腸同源病的診斷和治療相關問題介紹如下.
장도신경계통병변시만성소인편비적중요원인,저사병변포괄선천성거결장,야포괄거결장동원병,여절세포불성숙、절세포감소증급장신경원발육불량증등.목전대동원병적병인、진단급치료방식상유엄범적쟁의화불학정성,현대거결장동원병적진단화치료상관문제개소여하.
Enteric nervous system abnormalities are the main cause of severe chronic constipation in children.These abnormalities are collectively known as intestinal dysganglionosis,including Hirschsprung's disease (HD),and Hirschsprung's disease allied disorders(HAD) such as immature ganglion,hypoganglionosis(HG) and intestinal neuronal dysplasia(IND).HD and HAD have similar clinical manifestations,and accurate diagnosis is challenging.In this paper,difficulties in diagnosis and treatment of HAD are introduced.
