CAJ | 학술논문

与moyamoya病相比，moyamoya综合征尚未形成典型的异常血管网，moyamoya综合征中颅内动脉狭窄可能是moyamoya病的一个亚型或早期表现，且与moyamoya病存在相同的病理生理学机制。甲状腺功能亢进相关的moyamoya综合征的病理生理学机制包括自身免疫性破坏、血流动力学异常、动脉粥样硬化及交感神经兴奋性增加等，诊断和治疗上，应密切关注甲状腺素水平的变化。本文对甲状腺功能亢进相关的moyamoya综合征的病理生理学机制及临床诊断治疗中应注意的问题做一综述。
여moyamoya병상비，moyamoya종합정상미형성전형적이상혈관망，moyamoya종합정중로내동맥협착가능시moyamoya병적일개아형혹조기표현，차여moyamoya병존재상동적병리생이학궤제。갑상선공능항진상관적moyamoya종합정적병리생이학궤제포괄자신면역성파배、혈류동역학이상、동맥죽양경화급교감신경흥강성증가등，진단화치료상，응밀절관주갑상선소수평적변화。본문대갑상선공능항진상관적moyamoya종합정적병리생이학궤제급림상진단치료중응주의적문제주일종술。
The abnormal vascular network found in moyamoya syndrome is different from that in moyamoya disease. Stenosis in intracranial vessels found in moyamoya syndrome may be a subtype or an early stage of moyamoya disease. The pathophysiology in moyamoya syndrome may have some common ground with moyamoya disease. The pathophysiology in moyamoya syndrome associated with hyperthyroidism includes autoimmune disorder, abnormal hemodynamic, arteriosclerosis and increased sympathetic activation. Changes in thyroxin level should be concerned in clinical practice. In this review, we summarize the pathophysiology of moyamoya syndrome associated with hyperthyroidism and some points in clinical diagnosis and treatment.