CAJ | 학술논문

目的：分析颅内血管外皮细胞瘤颅外多器官转移的临床特点，以提高诊治水平。方法回顾分析1例颅内血管外皮细胞瘤8a间的回访资料，根据临床表现、影像学表现、手术治疗及放射治疗效果及转移情况，结合文献探讨其临床特点。结果颅内血管外皮细胞瘤患者术前影像与脑膜瘤不易区别，导致误诊。术中见脑膜有明显侵犯，血供丰富。术后病理需免疫组化确诊。术后随访期内发生原位复发及颅内附近转移和颅外多发转移。结论颅内血管外皮细胞瘤发生颅外多发转移较为罕见，需与脑膜瘤、孤立性纤维瘤鉴别。治疗以手术切除为首选，术后应常规行放疗，复发时可再次放疗并需定期随访。
목적：분석로내혈관외피세포류로외다기관전이적림상특점，이제고진치수평。방법회고분석1례로내혈관외피세포류8a간적회방자료，근거림상표현、영상학표현、수술치료급방사치료효과급전이정황，결합문헌탐토기림상특점。결과로내혈관외피세포류환자술전영상여뇌막류불역구별，도치오진。술중견뇌막유명현침범，혈공봉부。술후병리수면역조화학진。술후수방기내발생원위복발급로내부근전이화로외다발전이。결론로내혈관외피세포류발생로외다발전이교위한견，수여뇌막류、고립성섬유류감별。치료이수술절제위수선，술후응상규행방료，복발시가재차방료병수정기수방。
Objective To analyze the clinical features of intracranial hemangiopericytoma associated with extracranial mul‐tiple organ metastases ,and improve diagnosis and treatment .Methods The clinical manifestations ,imaging findings ,surgery and radiation therapy effect and metastasis of intracranial hemangiopericytoma were reviewed in one patient in 8 years ,the clini‐cal features of this kind of disease combining literatures were explored .Results The preoperative images of this patient and meningioma were not easy to distinguish and misdiagnosis easily .The significant meninges invasion and rich blood supply were observed in operation .Postoperative pathological diagnosis required immune‐histochemistry .Postoperative recurrence in situ and intracranial and extracranial multiple metastases were observed in follow‐up period .Conclusion The extracranial multiple organ metastasis of intracranial hemangiopericytoma is rare relatively .Intracranial hemangiopericytoma must be identification with meningioma and solitary fibrous tumor .Surgical resection is the preferred treatment and postoperative radiation therapy should be performed routinely .Radiotherapy can be done again when tumor relapse and regular follow‐up is necessary to this kind of disease .