CAJ | 학술논문

目的：探讨胚胎发育不良性神经上皮瘤（DNET）的CT及MRI表现特点。方法回顾性分析经病理证实的7例DNET患者的临床及影像学资料，对肿瘤的位置、形态、大小、边界、瘤周水肿、占位效应、密度／信号特点、有无强化等进行分析。结果7例DNET均位于幕上，其中额叶皮层及皮层下3例，颞叶深部海马区2例，侧脑室1例，边缘叶隔区1例。病灶边界清晰，无明显瘤周水肿及占位效应。CT为低密度；MRI表现为长T1长T2信号，病灶中有细线样分隔2例，“倒三角征”3例，“环形征”5例，轻度强化3例，DWI低信号3例。结论位于幕上皮层或皮层下、边界清晰、呈长T1长T2信号、呈“倒三角征”或“环形征”、DWI低信号、强化少见、无瘤周水肿及占位效应等特点有助于DNET的诊断，但亦需注意其不典型表现，以免误诊、漏诊。
목적：탐토배태발육불량성신경상피류（DNET）적CT급MRI표현특점。방법회고성분석경병리증실적7례DNET환자적림상급영상학자료，대종류적위치、형태、대소、변계、류주수종、점위효응、밀도／신호특점、유무강화등진행분석。결과7례DNET균위우막상，기중액협피층급피층하3례，섭협심부해마구2례，측뇌실1례，변연협격구1례。병조변계청석，무명현류주수종급점위효응。CT위저밀도；MRI표현위장T1장T2신호，병조중유세선양분격2례，“도삼각정”3례，“배형정”5례，경도강화3례，DWI저신호3례。결론위우막상피층혹피층하、변계청석、정장T1장T2신호、정“도삼각정”혹“배형정”、DWI저신호、강화소견、무류주수종급점위효응등특점유조우DNET적진단，단역수주의기불전형표현，이면오진、루진。
Objective To analyze the CT and MRI features of dysembryoplastic neuroepithelial tumors (DNET). Methods The CT and MRI studies of 7 patients with histologically confirmed DNET were reviewed retrospectively..The lesion location, morphology, size, border, peritumoral edema, mass effect, characters of density and signal intensity and contrast enhancement were analyzed. Results All of the 7 DNET located in supratentorial, 3 located in frontal lobe, 2 in deep of temporal lobe, 1 in lateral ventricle and 1 in septal area of limbic lobe..The lesions were all well-defined,.without peritumoral edema or mass effect. They displayed low density on CT without contrast enhancement..The MRI showed hypointense on T1WI and hyperintense on T2WI, 2 of them with filament septation,.3 with“reversed triangle sign”,.5 with“hyperintense ring sign”,.and 3 with slightly enhancement.. All the 3 DWI scans showed low signal intensity. Conclusion In supratentorial cortical or subcortical area,.well-defined margin, hypointense on T1WI and hyperintense on T2WI, “reversed triangle sign”, “hyperintense ring sign” on FLAIR, no peritumoral edema,.and no mass effect are helpful to the diagnosis of DNET..However,.it's important to pay attention to the atypical characteristics so as to avoid misdiagnosis.