CAJ | 학술논문

凝血因子Ⅶ（FⅦ）参与外源性凝血途径，是外源性凝血途径的重要启动因子之一。先天性FⅦ缺乏症是一种罕见的常染色体不完全隐性遗传性疾病。本文报道了1例先天性FⅦ缺乏症合并宫内占位患者的临床诊治经过，并结合文献复习，探讨该类疾病的诊断、治疗及预后。
응혈인자Ⅶ（FⅦ）삼여외원성응혈도경，시외원성응혈도경적중요계동인자지일。선천성FⅦ결핍증시일충한견적상염색체불완전은성유전성질병。본문보도료1례선천성FⅦ결핍증합병궁내점위환자적림상진치경과，병결합문헌복습，탐토해류질병적진단、치료급예후。
Coagulation factor Ⅶ( FⅦ)is an important promoter for extrinsic coagulation pathway. Congenital FⅦdeficiency is a rare autosomal recessive disorder. A case of congenital coagulation FⅦdeficiency complicated by space occupying lesion of the uterus was reported. The clinical diagnosis and treatment of the case were reported,and relevant literature view was also made. The diagnosis,treatment and prognosis of the disease were investigated.