临床眼科杂志
臨床眼科雜誌
림상안과잡지
JOURNAL OF CLINICAL OPHTHALMOLOGY
2015年
2期
105-107
,共3页
马建民%李金茹%葛心%王霄娜%刘骁
馬建民%李金茹%葛心%王霄娜%劉驍
마건민%리금여%갈심%왕소나%류효
眼眶病%特发性眼眶炎性假瘤%IgG4相关性疾病
眼眶病%特髮性眼眶炎性假瘤%IgG4相關性疾病
안광병%특발성안광염성가류%IgG4상관성질병
Orbital disease%Idiopathic orbital inflammatory pseudotumor%IgG4
目的:通过检测特发性眼眶炎性假瘤( IOIP)患者血清中IgG、IgG1、IgG2、IgG3和IgG4的水平,探究IgG及其亚型与特发性眼眶炎性假瘤发病之间的关系。方法回顾性病例系列研究。回顾性分析首都医科大学附属北京同仁医院眼肿瘤专科2013年1月至2014年12月间经病理组织学确诊的44例IOIP患者的血清学检测结果,研究其IgG、IgG1、IgG2、IgG3和IgG4的血清学水平。结果血清学分析IgG水平为(1211.9±337.7) mg/dL,44例中3例IgG升高,约占6.8%,1例IgG下降,约占2.3%;IgG1水平为(625.6±267.4) mg/dL,44例中4例IgG1升高,占9.1%,4例IgG1下降,占9.1%;IgG2水平为(535.6±221.2) mg/dL,44例中5例IgG2升高,2例下降,分别占11.4%和4.5%;IgG3水平为(54.4±30.7) mg/dL,44例中4例IgG3下降,约占9.1%;IgG4水平为(107.8±247.5) mg/dL,44例中16例IgG4升高,占36.4%,IgG4/IgG比值约为8.9%。结论超过三分之一的IOIP患者血清IgG4升高,且IgG4/IgG比值高于正常水平,提示部分IOIP属于IgG4相关性疾病。
目的:通過檢測特髮性眼眶炎性假瘤( IOIP)患者血清中IgG、IgG1、IgG2、IgG3和IgG4的水平,探究IgG及其亞型與特髮性眼眶炎性假瘤髮病之間的關繫。方法迴顧性病例繫列研究。迴顧性分析首都醫科大學附屬北京同仁醫院眼腫瘤專科2013年1月至2014年12月間經病理組織學確診的44例IOIP患者的血清學檢測結果,研究其IgG、IgG1、IgG2、IgG3和IgG4的血清學水平。結果血清學分析IgG水平為(1211.9±337.7) mg/dL,44例中3例IgG升高,約佔6.8%,1例IgG下降,約佔2.3%;IgG1水平為(625.6±267.4) mg/dL,44例中4例IgG1升高,佔9.1%,4例IgG1下降,佔9.1%;IgG2水平為(535.6±221.2) mg/dL,44例中5例IgG2升高,2例下降,分彆佔11.4%和4.5%;IgG3水平為(54.4±30.7) mg/dL,44例中4例IgG3下降,約佔9.1%;IgG4水平為(107.8±247.5) mg/dL,44例中16例IgG4升高,佔36.4%,IgG4/IgG比值約為8.9%。結論超過三分之一的IOIP患者血清IgG4升高,且IgG4/IgG比值高于正常水平,提示部分IOIP屬于IgG4相關性疾病。
목적:통과검측특발성안광염성가류( IOIP)환자혈청중IgG、IgG1、IgG2、IgG3화IgG4적수평,탐구IgG급기아형여특발성안광염성가류발병지간적관계。방법회고성병례계렬연구。회고성분석수도의과대학부속북경동인의원안종류전과2013년1월지2014년12월간경병리조직학학진적44례IOIP환자적혈청학검측결과,연구기IgG、IgG1、IgG2、IgG3화IgG4적혈청학수평。결과혈청학분석IgG수평위(1211.9±337.7) mg/dL,44례중3례IgG승고,약점6.8%,1례IgG하강,약점2.3%;IgG1수평위(625.6±267.4) mg/dL,44례중4례IgG1승고,점9.1%,4례IgG1하강,점9.1%;IgG2수평위(535.6±221.2) mg/dL,44례중5례IgG2승고,2례하강,분별점11.4%화4.5%;IgG3수평위(54.4±30.7) mg/dL,44례중4례IgG3하강,약점9.1%;IgG4수평위(107.8±247.5) mg/dL,44례중16례IgG4승고,점36.4%,IgG4/IgG비치약위8.9%。결론초과삼분지일적IOIP환자혈청IgG4승고,차IgG4/IgG비치고우정상수평,제시부분IOIP속우IgG4상관성질병。
Objective To analyze the serum levels of IgG, IgG1, IgG2, IgG3 and IgG4 in patients with idiopathic orbital inflammatory pseudotumor ( IOIP), and to investigate the relationship between the IOIP and Serum IgG Series. Methods This is a retrospective case series study.Author collected records of 44 patients with IOIP diagnosed pathologi-cally from Jan 2013 to Dec 2014 in Ocular Tumor Department of Beijing Tongren Hospital, Capital Medical University, and analyzed the serum levels of IgG, IgG1, IgG2, IgG3 and IgG4 in these patients.Results The average serum IgG was 1211.9 ±337.7 mg/dL.IgG was elevated in 3 patients (6.8%) and low in 1 patient (2.3%).The average serum IgG1 was 625.6 ±267.4 mg/dL.It was elevated in 4 patients (9.1%) and low in 4 patients (9.1%).The average serum IgG2 was 535.6 ±221.2 mg/dL.It was elevated in 5 patients (11.4%) and low in 2 patients (4.5%).The average serum IgG3 was 54.4 ±30.7 mg/dL.It was low in 4 patients (9.1%).The average serum IgG4 was 107.8 ±247.5 mg/dL.It was elevated in 16 patients (36.4%), and the ratio of IgG4/IgG was 8.9%in these patients.Conclusion Serum IgG4 level and IgG4/IgG ratio in patients with IOIP were higher than normal, suggesting that IOIP is related to mechanisms that involve IgG4.