安徽医药
安徽醫藥
안휘의약
ANHUI MEDICAL AND PHARMACEUTICAL JOURNAL
2015年
4期
706-708,709
,共4页
骨肿瘤%血管肉瘤%上皮样血管肉瘤%免疫组化
骨腫瘤%血管肉瘤%上皮樣血管肉瘤%免疫組化
골종류%혈관육류%상피양혈관육류%면역조화
bone neoplasms%angiosarcoma%epithelioid angiosarcoma%immunohistochemical
目的:探讨骨原发上皮样血管肉瘤( PEAB)的临床病理特点。方法报道1例骨原发上皮样血管肉瘤临床资料、组织学及免疫组化染色结果及随访结果。结果该例骨原发上皮样血管肉瘤的临床症状为局部疼痛,查体发现局部压痛,镜下示上皮样肿瘤细胞排列成假腺样、乳头状,可见原始血管结构形成。免疫组化显示瘤细胞高表达CD31、CKpan、Vimentin,并表达CD34,而EMA、SMA、S-100、Myogenin及HMB45等均阴性。结论骨的原发上皮样血管肉瘤罕见,其组织结构极易被误诊为转移癌,诊断需结合临床及影像学资料,对组织病理学的详细观察及免疫组化染色的协助,对于正确诊断和鉴别诊断有重要意义。
目的:探討骨原髮上皮樣血管肉瘤( PEAB)的臨床病理特點。方法報道1例骨原髮上皮樣血管肉瘤臨床資料、組織學及免疫組化染色結果及隨訪結果。結果該例骨原髮上皮樣血管肉瘤的臨床癥狀為跼部疼痛,查體髮現跼部壓痛,鏡下示上皮樣腫瘤細胞排列成假腺樣、乳頭狀,可見原始血管結構形成。免疫組化顯示瘤細胞高錶達CD31、CKpan、Vimentin,併錶達CD34,而EMA、SMA、S-100、Myogenin及HMB45等均陰性。結論骨的原髮上皮樣血管肉瘤罕見,其組織結構極易被誤診為轉移癌,診斷需結閤臨床及影像學資料,對組織病理學的詳細觀察及免疫組化染色的協助,對于正確診斷和鑒彆診斷有重要意義。
목적:탐토골원발상피양혈관육류( PEAB)적림상병리특점。방법보도1례골원발상피양혈관육류림상자료、조직학급면역조화염색결과급수방결과。결과해례골원발상피양혈관육류적림상증상위국부동통,사체발현국부압통,경하시상피양종류세포배렬성가선양、유두상,가견원시혈관결구형성。면역조화현시류세포고표체CD31、CKpan、Vimentin,병표체CD34,이EMA、SMA、S-100、Myogenin급HMB45등균음성。결론골적원발상피양혈관육류한견,기조직결구겁역피오진위전이암,진단수결합림상급영상학자료,대조직병이학적상세관찰급면역조화염색적협조,대우정학진단화감별진단유중요의의。
Objective To investigate the clinicopathological characteristics,diagnosis and differential diagnosis,treatment and prognosis of primary epithelioid angiosarcoma in bone PEAB.Methods One case of PEAB was retrospectively reviewed on the clinical data,his-tological and immunohistochemical features,the follow-up,and the related literature.Results The symptom of the case was localized pain.Physical examination results showed that there was local tenderness.Histologically,PEAB was comprised of the epithelioid-like cells arranged in pseudoglandular or papillary patterns.Structure of primitive vascular can be seen in some areas.Immunohistochemical-ly,the tumor cells were stained positive for CD31,CK,vimentin and CD34,negative for SMA,S-100,EMA,Myogenin and HMB45.Con-clusions PEAB is very rare.Because of its histopathological character,it is likely to be misdiagnosed as metastatic carcinoma.An ac-curate diagnosis is based on clinical manifestations,imaging,histopathological test and immunohistochemical staining.