CAJ | 학술논문

Ⅰ型先天性胆管扩张症也称先天性胆总管囊囊肿(CCC),是一种先天性胆道缺陷性疾病.内镜超声(EUS)、磁共振胆管胰造影(MRCP)和内镜逆行胰胆管造影(ERCP)等影像学检查对本病诊断具有极其重要的作用.手术是该病主要治疗手段.而“胆囊切除+胆总管囊肿完整切除+肝总管空肠Roux-Y吻合术”是首选术式.本文综述了该病原因、分类、诊断及治疗进展.
Ⅰ형선천성담관확장증야칭선천성담총관낭낭종(CCC),시일충선천성담도결함성질병.내경초성(EUS)、자공진담관이조영(MRCP)화내경역행이담관조영(ERCP)등영상학검사대본병진단구유겁기중요적작용.수술시해병주요치료수단.이“담낭절제+담총관낭종완정절제+간총관공장Roux-Y문합술”시수선술식.본문종술료해병원인、분류、진단급치료진전.
Type Ⅰ congenital biliary dilatation is a congenital biliary duct defect disease.It is also called congenital choledochocele cyst (CCC).Endoscopic ultrasonography (EUS),magnetic resonance cholangiopacreatography (MRCP) and endoscopic retrograde cholangiopancreatography (ERCP) are very important for the diagnosis.Operation is generally regaded as the best choose.It is recommended that "cholecystectomy + choledochal cyst excision + hepatic duct jejunum Roux-Y anastomosis" is the chief therapeutic method.This article reviews the pathogenesis,classifications,diagnosis and treatment of the disease.