临床外科杂志
臨床外科雜誌
림상외과잡지
JOURNAL OF CLINICAL SURGERY
2015年
5期
364-365
,共2页
陈星%林钟轩%陈玉华%吴鸿念%蔡霖%刘加夫
陳星%林鐘軒%陳玉華%吳鴻唸%蔡霖%劉加伕
진성%림종헌%진옥화%오홍념%채림%류가부
淀粉样变%支气管%肺%诊断%治疗%预后
澱粉樣變%支氣管%肺%診斷%治療%預後
정분양변%지기관%폐%진단%치료%예후
amyloidosis%bronchial%pulmonary%diagnosis%treatment%prognosis
目的:探讨原发性支气管肺淀粉样变性临床表现、诊断、治疗及预后。方法回顾性分析10例原发性支气管肺淀粉样变性患者的临床特点。结果原发性支气管肺淀粉样变性患者临床表现为咳嗽、咳痰、咯血、气促,可经纤维支气管镜、肺穿刺或胸腔镜手术活检病理检查确诊,刚果红染色阳性为典型病理特征。结论本病临床少见,病理检查为确诊金标准。目前无疗效确切的治疗药物,气管受累及弥漫性病变者预后差。
目的:探討原髮性支氣管肺澱粉樣變性臨床錶現、診斷、治療及預後。方法迴顧性分析10例原髮性支氣管肺澱粉樣變性患者的臨床特點。結果原髮性支氣管肺澱粉樣變性患者臨床錶現為咳嗽、咳痰、咯血、氣促,可經纖維支氣管鏡、肺穿刺或胸腔鏡手術活檢病理檢查確診,剛果紅染色暘性為典型病理特徵。結論本病臨床少見,病理檢查為確診金標準。目前無療效確切的治療藥物,氣管受纍及瀰漫性病變者預後差。
목적:탐토원발성지기관폐정분양변성림상표현、진단、치료급예후。방법회고성분석10례원발성지기관폐정분양변성환자적림상특점。결과원발성지기관폐정분양변성환자림상표현위해수、해담、각혈、기촉,가경섬유지기관경、폐천자혹흉강경수술활검병리검사학진,강과홍염색양성위전형병리특정。결론본병림상소견,병리검사위학진금표준。목전무료효학절적치료약물,기관수루급미만성병변자예후차。
Objective To study the manifestation,diagnosis,treatment and prognosis of the pri-mary bronchial and pulmonary amyloidosis.Methods The clinical features of 10 cases of primary bron-chial and pulmonary amyloidosis were summarized retrospectively.Results The most common symptoms of primary bronchial and pulmonary amyloidosis were coughing,sputum,anhelation,and emptysis.Its diag-nosis relied on fiberoptic bronchoscopy,lung puncture biopsy or VATS biopsy.Positive Congo red stain was the characteristic of pathology.Conclusion The primary bronchial and pulmonary amyloidosis is rare in clinical practice.Its diagnosis relies on pathology.There are no specific medicines for treatment so far.Pa-tient with tracheal involvement and diffuse lesions usually has a poor prognosis.