CAJ | 학술논문

儿童良性癫痫伴中央颞区棘波（ benign childhood epilepsy with centrotemporal spikes ，BECT）是儿童癫痫中最常见的癫痫综合征，其预后通常良好，但仍有部分BECT患儿可能在病程中出现负性肌阵挛、不典型失神、口部运动障碍、言语表达障碍等不典型表现，称为BECT变异型。这一部分患儿起病早，临床症状持续时间长，甚至发展成发作类型复杂的癫痫或癫痫综合征，其预后尤其是认知和精神心理方面并不乐观。因此临床医师应对BECT变异型正确认识，以进行早期准确预判，密切监测病情变化，确定正确的治疗方案并积极干预。
인동량성전간반중앙섭구극파（ benign childhood epilepsy with centrotemporal spikes ，BECT）시인동전간중최상견적전간종합정，기예후통상량호，단잉유부분BECT환인가능재병정중출현부성기진련、불전형실신、구부운동장애、언어표체장애등불전형표현，칭위BECT변이형。저일부분환인기병조，림상증상지속시간장，심지발전성발작류형복잡적전간혹전간종합정，기예후우기시인지화정신심리방면병불악관。인차림상의사응대BECT변이형정학인식，이진행조기준학예판，밀절감측병정변화，학정정학적치료방안병적겁간예。
Benign childhood epilepsy with centrotemporal spikes (BECTS) is a well-defined childhood epilepsy syn-drome that has generally been associated with a favorable prognosis.However,there is still a part of them that will develop into different atypical evolutions, such as negative myoclonus, atypical absences, oromotor dysfunction, and speech arrest etc.These are referred to as variants of benign childhood epilepsy with centrotemporal spikes.These atypical BECTS, which present in children at early age and as frequently prolonged seizures, are more prone to evolve into refractory seizures or epilepsy syndromes ,resulting in a worse prognosis especially due to the development of cognitive and other psychological hazards.Therefore, a better recognition of this disease, its early diagnosis and timely treatment will be important.