中华手外科杂志
中華手外科雜誌
중화수외과잡지
CHINESE JOURNAL OF HAND SURGERY
2015年
4期
245-248
,共4页
马炜%田文%赵俊会%田光磊%郭阳%于龙彪%刘波%殷耀斌%钟文耀
馬煒%田文%趙俊會%田光磊%郭暘%于龍彪%劉波%慇耀斌%鐘文耀
마위%전문%조준회%전광뢰%곽양%우룡표%류파%은요빈%종문요
Poland综合征%先天畸形%形态学特征%治疗策略
Poland綜閤徵%先天畸形%形態學特徵%治療策略
Poland종합정%선천기형%형태학특정%치료책략
Poland syndrome%Congenital abnormalities%Morphological characteristics%Treatment strategy
目的 研究和总结Poland综合征手和胸大肌以外的畸形临床形态学特征及治疗策略.方法 回顾分析自2000年2月至2014年4月我院收治的91例Poland综合征患者资料,对Poland综合征手和胸大肌以外的畸形进行定性的研究和总结,并探讨各类畸形的治疗方法.结果 91例中有85例发现存在除手部和胸部以外的畸形,其中71例存在2种或2种以上合并畸形.共发现12种合并畸形,前三位者分别为乳头发育异常、肋骨发育异常及锁骨短小畸形.结论 Poland综合征并非一局限性先天畸形,除手部和胸大肌畸形外,还有很多其他部位的畸形,严重影响患者的外观及功能.要求手外科医师对Poland综合征可能出现的形态学特征有更全面的了解,进行更为细致的检查,才能及时发现这些畸形,从而联合相应科室针对不同性别的患者在不同年龄段及时制定个体化治疗方案.
目的 研究和總結Poland綜閤徵手和胸大肌以外的畸形臨床形態學特徵及治療策略.方法 迴顧分析自2000年2月至2014年4月我院收治的91例Poland綜閤徵患者資料,對Poland綜閤徵手和胸大肌以外的畸形進行定性的研究和總結,併探討各類畸形的治療方法.結果 91例中有85例髮現存在除手部和胸部以外的畸形,其中71例存在2種或2種以上閤併畸形.共髮現12種閤併畸形,前三位者分彆為乳頭髮育異常、肋骨髮育異常及鎖骨短小畸形.結論 Poland綜閤徵併非一跼限性先天畸形,除手部和胸大肌畸形外,還有很多其他部位的畸形,嚴重影響患者的外觀及功能.要求手外科醫師對Poland綜閤徵可能齣現的形態學特徵有更全麵的瞭解,進行更為細緻的檢查,纔能及時髮現這些畸形,從而聯閤相應科室針對不同性彆的患者在不同年齡段及時製定箇體化治療方案.
목적 연구화총결Poland종합정수화흉대기이외적기형림상형태학특정급치료책략.방법 회고분석자2000년2월지2014년4월아원수치적91례Poland종합정환자자료,대Poland종합정수화흉대기이외적기형진행정성적연구화총결,병탐토각류기형적치료방법.결과 91례중유85례발현존재제수부화흉부이외적기형,기중71례존재2충혹2충이상합병기형.공발현12충합병기형,전삼위자분별위유두발육이상、륵골발육이상급쇄골단소기형.결론 Poland종합정병비일국한성선천기형,제수부화흉대기기형외,환유흔다기타부위적기형,엄중영향환자적외관급공능.요구수외과의사대Poland종합정가능출현적형태학특정유경전면적료해,진행경위세치적검사,재능급시발현저사기형,종이연합상응과실침대불동성별적환자재불동년령단급시제정개체화치료방안.
Objective To study and review the morphological characteristics of and treatment strategy for malformations other than hand and pectoralis major deformities in Poland syndrome.Methods Ninety-one cases of Poland syndrome treated from February 2000 to April 2014 were retrospectively reviewed.The clinical morphological characteristics of malformations other than hand and pectoralis major deformities were systemically analyzed,and the treatment methods of various malformations were also reviewed and summarized.Results Eighty-five out of the 91 cases had associating deformities other than the hand and chest.Seventy-one cases had 2 or more than 2 additional deformities.A total of 12 types of deformity existed,the top three being nipple,rib and clavicle deformities.Conclusion Morphological changes of patients with Poland syndrome are complex.Besides deformities in the hands and pectoralis major,there are deformities in other parts of the body,which can seriously affect the appearance and function.Hand surgeons should have a more comprehensive understanding of the morphological manifestations of Poland syndrome and thorough physical examination of the patient to make an individualized treatment plan teamed with relevant departments and based on gender and age of the patient.
