CAJ | 학술논문

目的：探讨肺淋巴管肌瘤病（pulmonary lymphangiomyomatosis，PLAM）的影像学诊断价值，以提高对本病的认识水平。方法收集2008年～2010年2例经临床影像综合诊断为肺淋巴管肌瘤病的临床及影像学资料加以回顾性分析。结果2例均为女性，都有进行性呼吸困难病史，CT表现为两肺广泛的薄壁含气囊腔，其中合并气胸1例，合并肺部感染1例。结论 PLAM的影像学表现具有某些特征性改变，尤其是高分辨率CT（HRCT），对该病的诊断具有重要作用。当患者为生育年龄的妇女，结合典型的临床资料和HRCT某些特征性改变，应高度怀疑本病。
목적：탐토폐림파관기류병（pulmonary lymphangiomyomatosis，PLAM）적영상학진단개치，이제고대본병적인식수평。방법수집2008년～2010년2례경림상영상종합진단위폐림파관기류병적림상급영상학자료가이회고성분석。결과2례균위녀성，도유진행성호흡곤난병사，CT표현위량폐엄범적박벽함기낭강，기중합병기흉1례，합병폐부감염1례。결론 PLAM적영상학표현구유모사특정성개변，우기시고분변솔CT（HRCT），대해병적진단구유중요작용。당환자위생육년령적부녀，결합전형적림상자료화HRCT모사특정성개변，응고도부의본병。
ObjectiveTo evaulate the value of imaging diagnosis of Pulmonary Lymphangiomyomatosis (PLAM) and to combine the review of literature,to improve the knowledge on this disease.MethodsClinical and imaging data in 2 patients with PLAM from 2008 to 2010 were restrospectively analyzed.ResultsAll 2 cases were female and gradually dyspnea. CT findings were widespread thin-wall airspace in the lungs.Among with pneumothorax, pulmonary infection each one.ConclusionImaging appearances of PLAM had a few characteristic changes,which especially is HRCT. PLAM is highly suspected if woman was bearing age, combined with typical clinic data and HRCT characteristic changes.