CAJ | 학술논문

目的：分析肾上腺Castleman病的临床特征及诊疗方法。方法对本院确诊的1例肾上腺Castleman病的临床和病理特点进行回顾性分析，并复习相关文献，总结该病的临床特点以及病因。结果该患者系体检发现肾上腺意外瘤，总结临床特征如下：(1)发病隐匿，表现为后腹膜巨大占位，伴有后腹膜淋巴结肿大；(2)无肾上腺功能异常；(3)术后病理证实为肾上腺Castleman病，透明血管型；(4)手术切除为首选治疗，局限性肾上腺Castleman病预后好。结论肾上腺Castleman病多以肾上腺区巨大占位为主要临床表现，对该病临床特征的深入了解，临床医师与病理医师的合作有助于临床早期诊断和治疗，避免漏诊或误诊。
목적：분석신상선Castleman병적림상특정급진료방법。방법대본원학진적1례신상선Castleman병적림상화병리특점진행회고성분석，병복습상관문헌，총결해병적림상특점이급병인。결과해환자계체검발현신상선의외류，총결림상특정여하：(1)발병은닉，표현위후복막거대점위，반유후복막림파결종대；(2)무신상선공능이상；(3)술후병리증실위신상선Castleman병，투명혈관형；(4)수술절제위수선치료，국한성신상선Castleman병예후호。결론신상선Castleman병다이신상선구거대점위위주요림상표현，대해병림상특정적심입료해，림상의사여병리의사적합작유조우림상조기진단화치료，피면루진혹오진。
Objective To raise the awareness of adrenal Castleman′s disease by analyzing the clinical features and management of a patient with adrenal Castleman′s disease. Methods A case of adrenal Castleman′s disease of our hospital was retrospectively analyzed, including clinical feature, laboratory findings, pathology, treatment, and follow-up. All the data and pertinent literatures were reviewed and analyzed. Results An incidentaloma measuring 4. 8 cm × 6. 3 cm in the right adrenal gland was observed in a 30-year-old men in a ultrasonography examination performed due to a medical check-up. Laboratory analysis showed that the lesion was not hyperfunctioning. The patient subsequently underwent an exploratory laparotomy. Pathological examination revealed retroperitoneally localized Castleman′s disease of the hyaline vascular type. Conclusion Adrenal Castleman′s disease is a rare cause of lymph node hypertrophy, and it is necessary to keep in mind the possibility of its occurrence and take it into consideration in the differential diagnosis of any solitary, heterogeneous, and hypervascular retroperitoneal mass. The proper cooperation between the clinician and pathologist allows early diagnosis and suitable therapy.