CAJ | 학술논문

Kaposi型血管内皮瘤是一种定义为中间型的血管肿瘤. 本文对1例发生于小肠系膜Kapo-si型血管内皮瘤患者的组织病理学、免疫表型及临床资料进行回顾性分析并文献复习. 该例患者以消化道出血为主要症状,影像学示肠系膜巨大软组织肿块并侵犯回肠,临床未见卡梅诺现象( Kasabach-mer-ritt phenomenon,KMP) ,光镜下可见海绵状脉管样结构,部分区域间质伴淋巴细胞聚集灶,其间散在较多由短梭形细胞瘤构成的结节,结节内瘤细胞呈纵横交错排列并形成条索或裂隙样血管. 免疫组化:CD31 (+),CD34(+),D2-40(+),C-Kit(-),SMA(-),Ki-67(1%).
Kaposi형혈관내피류시일충정의위중간형적혈관종류. 본문대1례발생우소장계막Kapo-si형혈관내피류환자적조직병이학、면역표형급림상자료진행회고성분석병문헌복습. 해례환자이소화도출혈위주요증상,영상학시장계막거대연조직종괴병침범회장,림상미견잡매낙현상( Kasabach-mer-ritt phenomenon,KMP) ,광경하가견해면상맥관양결구,부분구역간질반림파세포취집조,기간산재교다유단사형세포류구성적결절,결절내류세포정종횡교착배렬병형성조색혹렬극양혈관. 면역조화:CD31 (+),CD34(+),D2-40(+),C-Kit(-),SMA(-),Ki-67(1%).
Kaposiform hemangioendothelioma ( KHE ) is a vascular tumor characterized by intermediate malignancy.Retrospective analysis and literature review on the clinical pathologic,immunohistochemical and clini-cal data of a patient with mesentery KHE.The cardinal symptom of this patient is alimentary track hemorrhage, imageological diagnosed as a huge soft tissue mass of mesentery and invaded ileum.Clinical feature is without Ka-sabach-Merritt phenomenon,observing under the light microscope.The tumor is with cavernous vascular structure, and lymphocyte infiltration inside of stroma.The nodules are composed of disposed and lots of short spindle cell tumor;the tumor cells inside of the nodules are vertical and horizontal staggered and form tendon like or fissuring vessels.Immunohistochemistry:CD31(+),CD34(+),D2-40(+),C-Kit(-),SMA(-),Ki-67(1%).